Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI ThPP Metabolite kegg.compound:C00068 wikidata:Q415003 chebi:9532;chebi:9532 inchikey:AYEKOFBPNLCAJY-UHFFFAOYSA-O Pyruvate Metabolite kegg.compound:C00022 wikidata:Q213580 chebi:32816;chebi:15361;chebi:32816 inchikey:LCTONWCANYUPML-UHFFFAOYSA-N Isocitrate Metabolite kegg.compound:C00311 wikidata:Q288927 chebi:30887;chebi:30887 inchikey:ODBLHEXUDAPZAU-UHFFFAOYSA-N Acetyl-CoA Metabolite kegg.compound:C00024 wikidata:Q715317 chebi:15351;chebi:15351 inchikey:ZSLZBFCDCINBPY-ZSJPKINUSA-N 2-Hydroxy-ethyl-ThPP Metabolite kegg.compound:C05125 wikidata:Q27105387 chebi:978;chebi:978 inchikey:RRUVJGASJONMDY-UHFFFAOYSA-O Oxalosuccinate Metabolite kegg.compound:C05379 wikidata:Q424172 chebi:7815;chebi:44712;chebi:44712;chebi:7815 inchikey:UFSCUAXLTRFIDC-UHFFFAOYSA-N;inchikey:UFSCUAXLTRFIDC-REOHCLBHSA-N Citrate Metabolite kegg.compound:C00158 wikidata:Q159683 chebi:30769;chebi:16947;chebi:30769 inchikey:KRKNYBCHXYNGOX-UHFFFAOYSA-N Succinate Metabolite kegg.compound:C00042 wikidata:Q213050 chebi:15741;chebi:15741 inchikey:KDYFGRWQOYBRFD-UHFFFAOYSA-N Oxaloacetate Metabolite kegg.compound:C00036 wikidata:Q408658 chebi:30744;chebi:30744;chebi:16452 inchikey:KHPXUQMNIQBQEV-UHFFFAOYSA-N Dihydro-lipoamide-E Metabolite chebi:80219 chebi:80219 Lipoamide-E Metabolite kegg.compound:C15972 wikidata:Q61963483 chebi:80218;chebi:80218 3-carboxy-1-hydroxypropyl-ThPP Metabolite pubchem.compound:440649 wikidata:Q27105465 chebi:1463;chebi:1463 inchikey:ZWUKRGPVMMTMAF-UHFFFAOYSA-O Succinoyl-CoA Metabolite kegg.compound:C00091 wikidata:Q419560 chebi:15380;chebi:15380 inchikey:VNOYUJKHFWYWIR-ITIYDSSPSA-N Phosphoenol-pyruvate Metabolite kegg.compound:C00074 wikidata:Q412139 chebi:18021;chebi:44897;chebi:44897 inchikey:DTBNBXWJWCWCIK-UHFFFAOYSA-N (S)-Malate Metabolite kegg.compound:C00149 wikidata:Q27104150 chebi:30797;chebi:30797;chebi:15589 inchikey:BJEPYKJPYRNKOW-REOHCLBHSA-N 2-Oxo-glutarate Metabolite kegg.compound:C00026 wikidata:Q306140 chebi:30915;chebi:30915;chebi:16810 inchikey:KPGXRSRHYNQIFN-UHFFFAOYSA-N S-Succinyl-dihydrolipoamide-E Metabolite kegg.compound:C16254 chebi:80403 Fumarate Metabolite kegg.compound:C00122 wikidata:Q139857 chebi:18012;chebi:29806;chebi:18012 inchikey:VZCYOOQTPOCHFL-OWOJBTEDSA-N S-Acetyldihydro-lipoamide-E Metabolite kegg.compound:C16255 chebi:50623;chebi:50623;chebi:80404 inchikey:WXCOTNFMLYTGPZ-UHFFFAOYSA-N ThPP Metabolite kegg.compound:C00068 wikidata:Q415003 chebi:9532;chebi:9532 inchikey:AYEKOFBPNLCAJY-UHFFFAOYSA-O Dihydro-lipoamide-E Metabolite chebi:80219 chebi:80219 Lipoamide-E Metabolite kegg.compound:C15972 wikidata:Q61963483 chebi:80218;chebi:80218 DLST GeneProduct ensembl:ENSG00000119689 ensembl:ENSG00000119689 ncbigene:1743 hgnc.symbol:DLST uniprot:A0A024R6C9;uniprot:G3V5M3;uniprot:G3V3F0;uniprot:G3V5L9;uniprot:H0YJF9;uniprot:G3V498;uniprot:P36957;uniprot:B7ZAZ8;uniprot:Q86SW4 DLD GeneProduct ensembl:ENSG00000091140 ensembl:ENSG00000091140 ncbigene:1738 hgnc.symbol:DLD uniprot:F2Z2E3;uniprot:F8WDM5;uniprot:F8WDY5;uniprot:P09622;uniprot:E9PEX6;uniprot:A0A024R713 ACO1 GeneProduct ensembl:ENSG00000122729 ensembl:ENSG00000122729 ncbigene:48 hgnc.symbol:ACO1 uniprot:P21399;uniprot:V9HWB7 FH GeneProduct ensembl:ENSG00000091483 ensembl:ENSG00000091483 ncbigene:2271 hgnc.symbol:FH uniprot:P07954;uniprot:A0A0S2Z4C3 MDH1 GeneProduct ensembl:ENSG00000014641 ensembl:ENSG00000014641 ncbigene:4190 hgnc.symbol:MDH1 uniprot:C9IZI0;uniprot:B8ZZ51;uniprot:V9HWF2;uniprot:P40925;uniprot:B9A041;uniprot:C9JRL4;uniprot:C9JLV6;uniprot:F8WFC2;uniprot:A0A5K1VW95;uniprot:C9JF79 OGDH GeneProduct ensembl:ENSG00000105953 ensembl:ENSG00000105953 ncbigene:4967 hgnc.symbol:OGDH uniprot:A0A140VJQ5;uniprot:C9J4G7;uniprot:E9PCR7;uniprot:Q02218;uniprot:E9PFG7;uniprot:E9PDF2 IDH1 GeneProduct ensembl:ENSG00000138413 ensembl:ENSG00000138413 ncbigene:3417 hgnc.symbol:IDH1 uniprot:A0A024R3Y6;uniprot:C9JLU6;uniprot:O75874;uniprot:C9JJE5;uniprot:C9J4N6 PCK1 GeneProduct ensembl:ENSG00000124253 ensembl:ENSG00000124253 ncbigene:5105 hgnc.symbol:PCK1 uniprot:P35558 ACLY GeneProduct ensembl:ENSG00000131473 ensembl:ENSG00000131473 ncbigene:47 hgnc.symbol:ACLY uniprot:K7EIE7;uniprot:P53396;uniprot:A0A024R1T9;uniprot:K7ESG8;uniprot:A0A024R1Y2 IDH1 GeneProduct ensembl:ENSG00000138413 ensembl:ENSG00000138413 ncbigene:3417 hgnc.symbol:IDH1 uniprot:A0A024R3Y6;uniprot:C9JLU6;uniprot:O75874;uniprot:C9JJE5;uniprot:C9J4N6 CS GeneProduct ensembl:ENSG00000062485 ensembl:ENSG00000062485 ncbigene:1431 hgnc.symbol:CS uniprot:F8VTT8;uniprot:F8W0J2;uniprot:F8VU34;uniprot:A0A024RB75;uniprot:F8VWQ5;uniprot:H0YIC4;uniprot:F8VX68;uniprot:F8VR34;uniprot:F8VRP1;uniprot:F8W642;uniprot:H0YH82;uniprot:A0A0C4DGI3;uniprot:F8VVY4;uniprot:F8W1S4;uniprot:F8W4S1;uniprot:F8VZK9;uniprot:F8VPA1;uniprot:F8VRI6;uniprot:F8VX07;uniprot:B4DJV2;uniprot:F8VPF9;uniprot:O75390 SUCLG2 GeneProduct ensembl:ENSG00000172340 ensembl:ENSG00000172340 ncbigene:8801 hgnc.symbol:SUCLG2 uniprot:Q96I99;uniprot:E9PDQ8;uniprot:H0Y852 PDHA1 GeneProduct ensembl:ENSG00000131828 ensembl:ENSG00000131828 ncbigene:5160 hgnc.symbol:PDHA1 uniprot:P08559;uniprot:Q5JPT9;uniprot:A0A024RBX9;uniprot:Q5JPU1;uniprot:Q5JPU0;uniprot:Q5JPU3;uniprot:Q5JPU2 IDH3A GeneProduct ensembl:ENSG00000166411 ensembl:ENSG00000166411 ncbigene:3419 hgnc.symbol:IDH3A uniprot:P50213;uniprot:H0YLF8;uniprot:H0YNF8;uniprot:Q68D72;uniprot:H0YNF5;uniprot:A0A0G2JL95;uniprot:H0YL72;uniprot:H0YMY5;uniprot:H0YM46;uniprot:H0YL05;uniprot:H0YM64;uniprot:H0YMU3;uniprot:H0YKD0;uniprot:H0YLI6 SDHA GeneProduct ensembl:ENSG00000073578 ensembl:ENSG00000073578 ncbigene:6389 hgnc.symbol:SDHA uniprot:P31040;uniprot:D6REB7;uniprot:H0Y8X1;uniprot:D6RFM5;uniprot:H0Y8S2;uniprot:A0A024QZ30 PC GeneProduct ncbigene:5091 ensembl:ENSG00000173599 ncbigene:5091 hgnc.symbol:PC uniprot:A0A494C016;uniprot:P11498;uniprot:A0A494C101;uniprot:A0A494BZT5;uniprot:A0A494C0T2;uniprot:A0A024R5C5;uniprot:E9PRE7 DLAT GeneProduct ensembl:ENSG00000150768 ensembl:ENSG00000150768 ncbigene:1737 hgnc.symbol:DLAT uniprot:P10515;uniprot:E9PEJ4;uniprot:E9PKC7;uniprot:H0YDD4;uniprot:Q86YI5 OGDH GeneProduct ensembl:ENSG00000105953 ensembl:ENSG00000105953 ncbigene:4967 hgnc.symbol:OGDH uniprot:A0A140VJQ5;uniprot:C9J4G7;uniprot:E9PCR7;uniprot:Q02218;uniprot:E9PFG7;uniprot:E9PDF2 PDHA1 GeneProduct ensembl:ENSG00000131828 ensembl:ENSG00000131828 ncbigene:5160 hgnc.symbol:PDHA1 uniprot:P08559;uniprot:Q5JPT9;uniprot:A0A024RBX9;uniprot:Q5JPU1;uniprot:Q5JPU0;uniprot:Q5JPU3;uniprot:Q5JPU2 DLD GeneProduct ensembl:ENSG00000091140 ensembl:ENSG00000091140 ncbigene:1738 hgnc.symbol:DLD uniprot:F2Z2E3;uniprot:F8WDM5;uniprot:F8WDY5;uniprot:P09622;uniprot:E9PEX6;uniprot:A0A024R713