Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI oxygen Metabolite chebi:25805 "" wikidata:Q629;wikidata:Q81977184 chebi:25805;chebi:25805 inchikey:QVGXLLKOCUKJST-UHFFFAOYSA-N Fumarate Metabolite chebi:18012 "" wikidata:Q139857 chebi:18012;chebi:18012 inchikey:VZCYOOQTPOCHFL-OWOJBTEDSA-N L-malate Metabolite chebi:15589 "" wikidata:Q27098126 chebi:15589;chebi:15589 inchikey:BJEPYKJPYRNKOW-REOHCLBHSA-L FH GeneProduct ensembl:ENSG00000091483 "" ensembl:ENSG00000091483 ncbigene:2271 hgnc.symbol:FH uniprot:A0A804HI24;uniprot:A0A804HKE6;uniprot:P07954;uniprot:A0A804HL52;uniprot:A0A0S2Z4C3 EPAS1 GeneProduct ensembl:ENSG00000116016 "" ensembl:ENSG00000116016 ncbigene:2034 hgnc.symbol:EPAS1 uniprot:Q99814;uniprot:C9J9N2 SETD2 GeneProduct ensembl:ENSG00000181555 "" ensembl:ENSG00000181555 ncbigene:29072 hgnc.symbol:SETD2 uniprot:H7BXT4;uniprot:H7BZ93;uniprot:Q9BYW2;uniprot:H7C3H4;uniprot:C9JG86;uniprot:A0A1W2PPX9 TFE3 GeneProduct ensembl:ENSG00000068323 "" ensembl:ENSG00000068323 ncbigene:7030 hgnc.symbol:TFE3 uniprot:A0A024QZ23;uniprot:P19532 PRCC GeneProduct ensembl:ENSG00000143294 "" ensembl:ENSG00000143294 ncbigene:5546 hgnc.symbol:PRCC uniprot:A0A0S2Z456;uniprot:H0YE12;uniprot:Q92733;uniprot:H0Y679 CDKN1A GeneProduct ensembl:ENSG00000124762 "" ensembl:ENSG00000124762 ncbigene:1026 hgnc.symbol:CDKN1A uniprot:A0A024RCX5;uniprot:P38936 TFE3 GeneProduct ensembl:ENSG00000068323 "" ensembl:ENSG00000068323 ncbigene:7030 hgnc.symbol:TFE3 uniprot:A0A024QZ23;uniprot:P19532 SFPQ GeneProduct ensembl:ENSG00000116560 "" ensembl:ENSG00000116560 ncbigene:6421 hgnc.symbol:SFPQ uniprot:A0A384N5Z8;uniprot:H0Y9U2;uniprot:P23246;uniprot:H0Y9K7 TFE3 GeneProduct ensembl:ENSG00000068323 "" ensembl:ENSG00000068323 ncbigene:7030 hgnc.symbol:TFE3 uniprot:A0A024QZ23;uniprot:P19532 DVL2 GeneProduct ensembl:ENSG00000004975 "" ensembl:ENSG00000004975 ncbigene:1856 hgnc.symbol:DVL2 uniprot:I3L0M7;uniprot:I3L2N2;uniprot:I3L2W9;uniprot:O14641;uniprot:I3L0Z8 CTSK GeneProduct ensembl:ENSG00000143387 "" ensembl:ENSG00000143387 ncbigene:1513 hgnc.symbol:CTSK uniprot:A0A7I2V354;uniprot:A0A7I2V5Y6;uniprot:Q5QP40;uniprot:A0A7I2V4B1;uniprot:A0A7I2V5Y9;uniprot:A0A7I2V4B6;uniprot:A0A7I2YQX0;uniprot:A0A7I2V2M6;uniprot:A0A7I2V617;uniprot:P43235 BIRC7 GeneProduct ensembl:ENSG00000101197 "" ensembl:ENSG00000101197 ncbigene:79444 hgnc.symbol:BIRC7 uniprot:Q96CA5;uniprot:A8MTF4 DIAPH1 GeneProduct ensembl:ENSG00000131504 "" ensembl:ENSG00000131504 ncbigene:1729 hgnc.symbol:DIAPH1 uniprot:B4E2I7;uniprot:A0A2R8YEF8;uniprot:H7C2W8;uniprot:O60610;uniprot:A0A2R8Y5N1 HIF1A GeneProduct ensembl:ENSG00000100644 "" ensembl:ENSG00000100644 ncbigene:3091 hgnc.symbol:HIF1A uniprot:A8MYV6;uniprot:D0VY79;uniprot:Q16665 CTSK GeneProduct ensembl:ENSG00000143387 "" ensembl:ENSG00000143387 ncbigene:1513 hgnc.symbol:CTSK uniprot:A0A7I2V354;uniprot:A0A7I2V5Y6;uniprot:Q5QP40;uniprot:A0A7I2V4B1;uniprot:A0A7I2V5Y9;uniprot:A0A7I2V4B6;uniprot:A0A7I2YQX0;uniprot:A0A7I2V2M6;uniprot:A0A7I2V617;uniprot:P43235 TFEB GeneProduct ensembl:ENSG00000112561 "" ensembl:ENSG00000112561 ncbigene:7942 hgnc.symbol:TFEB uniprot:A0A024RCY3;uniprot:B1AKA9;uniprot:B0QYS7;uniprot:B1AKB1;uniprot:P19484;uniprot:A0A1B0GXL9;uniprot:B0QYS6;uniprot:A0A7I2YQR9;uniprot:B1AKB5;uniprot:B1AKB4;uniprot:B1AKB2;uniprot:Q709A9 TFEB GeneProduct ensembl:ENSG00000112561 "" ensembl:ENSG00000112561 ncbigene:7942 hgnc.symbol:TFEB uniprot:A0A024RCY3;uniprot:B1AKA9;uniprot:B0QYS7;uniprot:B1AKB1;uniprot:P19484;uniprot:A0A1B0GXL9;uniprot:B0QYS6;uniprot:A0A7I2YQR9;uniprot:B1AKB5;uniprot:B1AKB4;uniprot:B1AKB2;uniprot:Q709A9 COL21A1 GeneProduct ensembl:ENSG00000124749 "" ensembl:ENSG00000124749 ncbigene:81578 hgnc.symbol:COL21A1 uniprot:A6PVD9;uniprot:H0Y4C9;uniprot:Q96P44;uniprot:A0A158RFW1;uniprot:F5GZK2;uniprot:H0YDH6 CADM2 GeneProduct ensembl:ENSG00000175161 "" ensembl:ENSG00000175161 ncbigene:253559 hgnc.symbol:CADM2 uniprot:G3XHN4;uniprot:Q8N3J6 HIF1A GeneProduct ensembl:ENSG00000100644 "" ensembl:ENSG00000100644 ncbigene:3091 hgnc.symbol:HIF1A uniprot:A8MYV6;uniprot:D0VY79;uniprot:Q16665 EGLN1 GeneProduct ensembl:ENSG00000135766 "" ensembl:ENSG00000135766 ncbigene:54583 hgnc.symbol:EGLN1 uniprot:A0A590UJD6;uniprot:A0A590UJT7;uniprot:R4SCQ0;uniprot:A0A590UJZ0;uniprot:A0A590UJ78;uniprot:Q9GZT9 EGLN2 GeneProduct ensembl:ENSG00000269858 "" ensembl:ENSG00000269858 ncbigene:112398 hgnc.symbol:EGLN2 uniprot:M0R1A3;uniprot:Q96KS0;uniprot:M0QXM8;uniprot:M0R035;uniprot:M0R2X9;uniprot:M0R110;uniprot:A0A024R0R2;uniprot:M0QXR0;uniprot:A0A0C4DGR4;uniprot:M0R1L0;uniprot:M0R1W4;uniprot:M0R350;uniprot:M0R0Z6 EGLN3 GeneProduct ensembl:ENSG00000129521 "" ensembl:ENSG00000129521 ncbigene:112399 hgnc.symbol:EGLN3 uniprot:F8VR39;uniprot:Q9H6Z9;uniprot:F8W1G2;uniprot:G3V3M1 ELOC GeneProduct ensembl:ENSG00000154582 "" ensembl:ENSG00000154582 ncbigene:6921 hgnc.symbol:ELOC uniprot:E5RHG8;uniprot:Q15369;uniprot:A0A024R7Y5;uniprot:R4GMY8 ELOB GeneProduct ensembl:ENSG00000103363 "" ensembl:ENSG00000103363 ncbigene:6923 hgnc.symbol:ELOB uniprot:Q15370;uniprot:A0A0B4J296;uniprot:B8ZZU8;uniprot:A0A384MDL3;uniprot:I3L0M9 VHL GeneProduct ensembl:ENSG00000134086 "" ensembl:ENSG00000134086 ncbigene:7428 hgnc.symbol:VHL uniprot:P40337;uniprot:A0A024R2F2;uniprot:A0A0S2Z4K1 RBX1 GeneProduct ensembl:ENSG00000100387 "" ensembl:ENSG00000100387 ncbigene:9978 hgnc.symbol:RBX1 uniprot:P62877 CUL2 GeneProduct ensembl:ENSG00000108094 "" ensembl:ENSG00000108094 ncbigene:8453 hgnc.symbol:CUL2 uniprot:A0A0A0MTN0;uniprot:Q5T2B5;uniprot:Q5T2B7;uniprot:A0A140VKB1;uniprot:Q13617 ARNT GeneProduct ensembl:ENSG00000143437 "" ensembl:ENSG00000143437 ncbigene:405 hgnc.symbol:ARNT uniprot:A6NGV6;uniprot:P27540;uniprot:D6RDB3 ARNT2 GeneProduct ensembl:ENSG00000172379 "" ensembl:ENSG00000172379 ncbigene:9915 hgnc.symbol:ARNT2 uniprot:Q9HBZ2;uniprot:X5DQN9;uniprot:H0YKW1 CREBBP GeneProduct ensembl:ENSG00000005339 "" ensembl:ENSG00000005339 ncbigene:1387 hgnc.symbol:CREBBP uniprot:Q92793;uniprot:I3L466;uniprot:A0A1B0GUU0;uniprot:I3L3I5;uniprot:I3L0Q1;uniprot:I3L293 EP300 GeneProduct ensembl:ENSG00000100393 "" ensembl:ENSG00000100393 ncbigene:2033 hgnc.symbol:EP300 uniprot:A0A0U1RR87;uniprot:A0A669KB12;uniprot:Q09472 SLC2A1 GeneProduct ensembl:ENSG00000117394 "" ensembl:ENSG00000117394 ncbigene:6513 hgnc.symbol:SLC2A1 uniprot:P11166;uniprot:A0A6Q8PFI8;uniprot:A0A0D9SFK9;uniprot:A0A0D9SG74;uniprot:A0A1W2PQ59;uniprot:A6NL68 VEGFA GeneProduct ensembl:ENSG00000112715 "" ensembl:ENSG00000112715 ncbigene:7422 hgnc.symbol:VEGFA uniprot:A0A0A0MTB2;uniprot:A0A0A0MSI7;uniprot:A0A0Y0IMM4;uniprot:A0A0A0MSH7;uniprot:H3BLW8;uniprot:A0A024RD33;uniprot:A0A0A0MSH5;uniprot:J3KPA4;uniprot:A0A024RD37;uniprot:A0A0A0MRQ4;uniprot:A0A5F9ZH41;uniprot:H0YBI8;uniprot:A2A2V4;uniprot:A0A0A0MR43;uniprot:P15692;uniprot:H0YBZ0 TGFB1 GeneProduct ensembl:ENSG00000105329 "" ensembl:ENSG00000105329 ncbigene:7040 hgnc.symbol:TGFB1 uniprot:A0A7I2V5Z9;uniprot:A0A499FJK2;uniprot:A0A7I2YQL8 TGFB2 GeneProduct ensembl:ENSG00000092969 "" ensembl:ENSG00000092969 ncbigene:7042 hgnc.symbol:TGFB2 uniprot:P61812 TGFB3 GeneProduct ensembl:ENSG00000119699 "" ensembl:ENSG00000119699 ncbigene:7043 hgnc.symbol:TGFB3 uniprot:A0A6Q8PGK5;uniprot:A5YM40;uniprot:P10600 PDGFB GeneProduct ensembl:ENSG00000100311 "" ensembl:ENSG00000100311 ncbigene:5155 hgnc.symbol:PDGFB uniprot:A9UJP0;uniprot:P01127;uniprot:A0A384NYY3;uniprot:A9UJN9 TGFA GeneProduct ensembl:ENSG00000163235 "" ensembl:ENSG00000163235 ncbigene:7039 hgnc.symbol:TGFA uniprot:P01135;uniprot:E7EPT6;uniprot:F8VNR3;uniprot:F8WA74;uniprot:H0Y6S5