Label	Type	Identifier	Comment	Ensembl	NCBI gene	HGNC	UniProt	Wikidata	ChEBI	InChI
hydroxylysine	Metabolite	chebi:60175	""					wikidata:Q27104861	chebi:60175;chebi:60175	inchikey:YSMODUONRAFBET-UHFFFAOYSA-N
Tryptophan	Metabolite	chebi:16828	""					wikidata:Q181003	chebi:16828;chebi:16828	inchikey:QIVBCDIJIAJPQS-VIFPVBQESA-N
Glutaric acid	Metabolite	chebi:17859	""					wikidata:Q409622	chebi:17859;chebi:17859	inchikey:JFCQEDHGNNZCLN-UHFFFAOYSA-N
Glutaconyl coenzyme A	Metabolite	chebi:57353	"AKA trans-4-carboxybut-2-enoyl-CoA"					wikidata:Q27124453	chebi:57353;chebi:57353	inchikey:URTLOTISFJPPOU-DEGQQWIJSA-I
3-Hydroxyglutaric acid	Metabolite	chebi:39980	""					wikidata:Q17048419	chebi:39980;chebi:39980	inchikey:ZQHYXNSQOIDNTL-UHFFFAOYSA-N
FAD	Metabolite	chebi:16238	""					wikidata:Q28746	chebi:16238;chebi:16238	inchikey:VWWQXMAJTJZDQX-UYBVJOGSSA-N
NADPH	Metabolite	chebi:16474	""					wikidata:Q26841327	chebi:16474;chebi:16474	inchikey:ACFIXJIJDZMPPO-NNYOXOHSSA-N
Acetyl coenzyme A	Metabolite	chebi:15351	""					wikidata:Q715317	chebi:15351;chebi:15351	inchikey:ZSLZBFCDCINBPY-ZSJPKINUSA-N
glutaryl-coenzyme A	Metabolite	chebi:15524	""					wikidata:Q3066713	chebi:15524;chebi:15524	inchikey:SYKWLIJQEHRDNH-CKRMAKSASA-N
L-2-Aminoadipic acid	Metabolite	chebi:37024	""					wikidata:Q2823204	chebi:37024;chebi:37024	inchikey:OYIFNHCXNCRBQI-UHFFFAOYSA-N
FADH2	Metabolite	chebi:17877	""					wikidata:Q27102690	chebi:17877;chebi:17877	inchikey:YPZRHBJKEMOYQH-UYBVJOGSSA-N
Glutaconic acid	Metabolite	chebi:24309	""					wikidata:Q27109839	chebi:24309;chebi:24309	inchikey:XVOUMQNXTGKGMA-UHFFFAOYSA-N
NADPH+	Metabolite	hmdb:HMDB0000221	""						chebi:16474;chebi:16474	inchikey:ACFIXJIJDZMPPO-NNYOXOHSSA-N
L-2-Hydroxyglutaric acid	Metabolite	hmdb:HMDB0000694	""						chebi:32797;chebi:32797	inchikey:HWXBTNAVRSUOJR-VKHMYHEASA-N
NADH	Metabolite	chebi:16908	""					wikidata:Q26987453	chebi:16908;chebi:16908	inchikey:BOPGDPNILDQYTO-NNYOXOHSSA-N
2-Oxoadipic acid	Metabolite	chebi:15753	""					wikidata:Q2823207	chebi:15753;chebi:15753	inchikey:FGSBNBBHOZHUBO-UHFFFAOYSA-N
L-N-Acetylaspartate	Metabolite	chebi:21547	""					wikidata:Q2629377	chebi:21547;chebi:21547	inchikey:OTCCIMWXFLJLIA-BYPYZUCNSA-N
H+	Metabolite	chebi:15378	""					wikidata:Q506710	chebi:15378;chebi:15378	inchikey:GPRLSGONYQIRFK-UHFFFAOYSA-N
Aspartate	Metabolite	chebi:17053	""					wikidata:Q178450	chebi:17053;chebi:17053	inchikey:CKLJMWTZIZZHCS-REOHCLBHSA-N
Coenzyme A	Metabolite	chebi:15346	""					wikidata:Q407635	chebi:15346;chebi:15346	inchikey:RGJOEKWQDUBAIZ-DRCCLKDXSA-N;inchikey:RGJOEKWQDUBAIZ-IBOSZNHHSA-N
lysine	Metabolite	chebi:25094	""					wikidata:Q178430	chebi:25094;chebi:25094	inchikey:KDXKERNSBIXSRK-UHFFFAOYSA-N
2-Ketoglutaric acid	Metabolite	chebi:30915	"AKA 2-ketoglutarate, 2-oxoglutarate, 2-oxopentanedioic acid, α-ketoglutarate"					wikidata:Q306140	chebi:30915;chebi:30915	inchikey:KPGXRSRHYNQIFN-UHFFFAOYSA-N
Crotonyl CoA	Metabolite	chebi:57332	"AKA (E)-but-2-enoyl-CoA"					wikidata:Q27124432	chebi:57332;chebi:57332	inchikey:KFWWCMJSYSSPSK-PAXLJYGASA-J
NAD+	Metabolite	chebi:15846	""					wikidata:Q26987253	chebi:15846;chebi:15846	inchikey:BAWFJGJZGIEFAR-NNYOXOHSSA-O
D-2-Hydroxyglutaric acid	Metabolite	chebi:15801	""					wikidata:Q27098238	chebi:15801;chebi:15801	inchikey:HWXBTNAVRSUOJR-GSVOUGTGSA-L
2-aminoadipic semialdehyde	Metabolite	chebi:61515	""					wikidata:Q27131118	chebi:61515;chebi:61515	inchikey:CRVYRJLIQHSUOQ-ZETCQYMHSA-N
Aspartate	Metabolite	chebi:17053	""					wikidata:Q178450	chebi:17053;chebi:17053	inchikey:CKLJMWTZIZZHCS-REOHCLBHSA-N
Acetyl coenzyme A	Metabolite	chebi:15351	""					wikidata:Q715317	chebi:15351;chebi:15351	inchikey:ZSLZBFCDCINBPY-ZSJPKINUSA-N
glutarylcarnitine	Metabolite	chebi:73040	""					wikidata:Q27140253	chebi:73040;chebi:73040	inchikey:NXJAXUYOQLTISD-UHFFFAOYSA-N
3-hydroxyglutaryl CoA	Metabolite	pubchem.compound:445127	""					wikidata:Q307532	chebi:15467;chebi:15467	inchikey:CABVTRNMFUVUDM-VRHQGPGLSA-N
Antiquitin	Protein	ensembl:ENSG00000164904	""	ensembl:ENSG00000164904	ncbigene:501	hgnc.symbol:ALDH7A1	uniprot:A0A1B0GW77;uniprot:A0A1B0GW65;uniprot:A0A1B0GTY9;uniprot:P49419;uniprot:A0A1B0GTG2;uniprot:A0A1B0GTJ4;uniprot:A0A0J9YWF7;uniprot:A0A1B0GV49;uniprot:H0YHM6;uniprot:A0A0J9YWM6;uniprot:A0A1B0GUA1;uniprot:A0A0J9YWK1;uniprot:F8WDY6;uniprot:A0A1B0GVU0;uniprot:A0A1B0GW82;uniprot:F8WD33;uniprot:A0A1B0GUY0;uniprot:F8VVF2			
IDH2	Protein	ensembl:ENSG00000182054	""	ensembl:ENSG00000182054	ncbigene:3418	hgnc.symbol:IDH2	uniprot:H0YL11;uniprot:P48735;uniprot:H0YLL5			
D-2-hydroxyglutarate dehydrogenase	Protein	uniprot:Q8N465	""	ensembl:ENSG00000180902	ncbigene:728294	hgnc.symbol:D2HGDH	uniprot:G5E9E8;uniprot:H7C290;uniprot:H7C3L2;uniprot:F8WCF9;uniprot:B5MCV2;uniprot:H7C0N1;uniprot:H7C021;uniprot:Q8N465			
L2HGDH	Protein	ensembl:ENSG00000087299	""	ensembl:ENSG00000087299	ncbigene:79944	hgnc.symbol:L2HGDH	uniprot:Q9H9P8;uniprot:C9JVN9;uniprot:G3V272;uniprot:G3V3E2;uniprot:G3V5S1			
L-malDH	Protein	uniprot:A0A024R4K3	""	ensembl:ENSG00000146701	ncbigene:4191	hgnc.symbol:MDH2	uniprot:U3KQ63;uniprot:A0A024R4K3;uniprot:G3XAL0;uniprot:P40926			
Hydroxyacid-oxoacid transhydrogenase	Protein	uniprot:B4DFI7	""	ensembl:ENSG00000147576	ncbigene:137872	hgnc.symbol:ADHFE1	uniprot:F2Z3E5;uniprot:F2Z2N0;uniprot:Q8IWW8;uniprot:F2Z3D8;uniprot:B4DV11;uniprot:B4DFI7			
Aminoacylase-2	Protein	uniprot:A0A1B0GTG3	"Aka ACY1"	ensembl:ENSG00000243989	ncbigene:95	hgnc.symbol:ACY1	uniprot:A0A1B0GU36;uniprot:F8WC59;uniprot:A0A1B0GVF7;uniprot:A0A1B0GU86;uniprot:C9JYZ0;uniprot:V9HWA0;uniprot:A0A1B0GTG3;uniprot:A0A1B0GUZ4;uniprot:A0A1B0GVG0;uniprot:A0A1B0GVZ3;uniprot:Q03154			
Glutaryl-CoA dehydrogenase	Protein	uniprot:Q92947	""	ensembl:ENSG00000105607	ncbigene:2639	hgnc.symbol:GCDH	uniprot:K7ES74;uniprot:K7EQ99;uniprot:K7ER63;uniprot:K7EKT3;uniprot:K7ERX1;uniprot:Q92947;uniprot:K7ESA6;uniprot:A0A024R7F9;uniprot:K7EKH1