Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI PubChem ChemSpider HMDB KEGG LipidMaps Hydroxylysine Metabolite chebi:60175 "" wikidata:Q27104861 chebi:60175 inchikey:YSMODUONRAFBET-UHFFFAOYSA-N pubchem.compound:1029 chemspider:1002 hmdb:HMDB0245508 Tryptophan Metabolite chebi:16828 "" wikidata:Q106345470;wikidata:Q181003 chebi:57912;chebi:16828 inchikey:QIVBCDIJIAJPQS-VIFPVBQESA-N pubchem.compound:6305;pubchem.compound:6923516 chemspider:6066 hmdb:HMDB0000929 kegg.compound:C00078 Glutaric acid Metabolite chebi:17859 "" wikidata:Q409622 chebi:17859 inchikey:JFCQEDHGNNZCLN-UHFFFAOYSA-N pubchem.compound:23322899;pubchem.compound:743 chemspider:723 hmdb:HMDB0000661 kegg.compound:C00489 lipidmaps:LMFA01170046 Glutaconyl coenzyme A Metabolite chebi:57353 "AKA trans-4-carboxybut-2-enoyl-CoA" wikidata:Q27124453 chebi:57353 inchikey:URTLOTISFJPPOU-DEGQQWIJSA-I pubchem.compound:45266582 chemspider:26330726 3-Hydroxyglutaric acid Metabolite chebi:39980 "" wikidata:Q17048419 chebi:39980 inchikey:ZQHYXNSQOIDNTL-UHFFFAOYSA-N pubchem.compound:181976 chemspider:158277 hmdb:HMDB0000428 FAD Metabolite chebi:16238 "" wikidata:Q28746 chebi:16238 inchikey:VWWQXMAJTJZDQX-UYBVJOGSSA-N pubchem.compound:643975 chemspider:559059 hmdb:HMDB0001248 kegg.compound:C00016 NADPH Metabolite chebi:16474 "" wikidata:Q26841327 chebi:16474 inchikey:ACFIXJIJDZMPPO-NNYOXOHSSA-N pubchem.compound:5884 chemspider:5673 hmdb:HMDB0000221 kegg.compound:C00005 Acetyl coenzyme A Metabolite chebi:15351 "" wikidata:Q715317 chebi:15351 inchikey:ZSLZBFCDCINBPY-ZSJPKINUSA-N pubchem.compound:444493 chemspider:392413 hmdb:HMDB0001206 kegg.compound:C00024 lipidmaps:LMFA07050281 glutaryl-coenzyme A Metabolite chebi:15524 "" wikidata:Q3066713 chebi:15524 inchikey:SYKWLIJQEHRDNH-CKRMAKSASA-N pubchem.compound:3081383 chemspider:2338999 hmdb:HMDB0001339 kegg.compound:C00527 lipidmaps:LMFA07050324 L-2-Aminoadipic acid Metabolite chebi:37024 "" wikidata:Q2823204 chebi:37024 inchikey:OYIFNHCXNCRBQI-UHFFFAOYSA-N pubchem.compound:59366488;pubchem.compound:469 chemspider:456 hmdb:HMDB0302754 kegg.compound:C00956 lipidmaps:LMFA01170098 FADH2 Metabolite chebi:17877 "" wikidata:Q27102690 chebi:17877 inchikey:YPZRHBJKEMOYQH-UYBVJOGSSA-N pubchem.compound:446013 chemspider:393487 hmdb:HMDB0001197 kegg.compound:C01352 Glutaconic acid Metabolite chebi:24309 "" wikidata:Q27109839 chebi:24309 inchikey:XVOUMQNXTGKGMA-UHFFFAOYSA-N pubchem.compound:74406 chemspider:66998 hmdb:HMDB0256281 NADPH+ Metabolite hmdb:HMDB0000221 "" chebi:16474 inchikey:ACFIXJIJDZMPPO-NNYOXOHSSA-N pubchem.compound:5884 chemspider:5673 hmdb:HMDB0000221 kegg.compound:C00005 L-2-Hydroxyglutaric acid Metabolite hmdb:HMDB0000694 "" chebi:32797 inchikey:HWXBTNAVRSUOJR-VKHMYHEASA-N pubchem.compound:439939 chemspider:388969 hmdb:HMDB0000694 kegg.compound:C03196 NADH Metabolite chebi:16908 "" wikidata:Q26987453 chebi:16908 inchikey:BOPGDPNILDQYTO-NNYOXOHSSA-N pubchem.compound:439153 chemspider:903;chemspider:388299 hmdb:HMDB0001487 kegg.compound:C00004 2-Oxoadipic acid Metabolite chebi:15753 "" wikidata:Q2823207 chebi:15753 inchikey:FGSBNBBHOZHUBO-UHFFFAOYSA-N pubchem.compound:71 chemspider:70 hmdb:HMDB0000225 kegg.compound:C00322 lipidmaps:LMFA01170121 L-N-Acetylaspartate Metabolite chebi:21547 "" wikidata:Q2629377 chebi:21547 inchikey:OTCCIMWXFLJLIA-BYPYZUCNSA-N pubchem.compound:65065 chemspider:58576;chemspider:88007 hmdb:HMDB0000812 kegg.compound:C01042 H⁺ Metabolite chebi:15378 "" wikidata:Q506710 chebi:15378 inchikey:GPRLSGONYQIRFK-UHFFFAOYSA-N pubchem.compound:1038 chemspider:1010 hmdb:HMDB0059597 kegg.compound:C00080 Aspartate Metabolite chebi:17053 "" wikidata:Q7226155;wikidata:Q178450 chebi:17053 inchikey:CKLJMWTZIZZHCS-REOHCLBHSA-N pubchem.compound:5960;pubchem.compound:139060126;pubchem.compound:44367445 chemspider:5745 hmdb:HMDB0000191 kegg.compound:C00049 Coenzyme A Metabolite chebi:15346 "" wikidata:Q407635 chebi:15346 inchikey:RGJOEKWQDUBAIZ-IBOSZNHHSA-N pubchem.compound:87642 chemspider:79067 hmdb:HMDB0001423 kegg.compound:C00010 Lysine Metabolite chebi:25094 "" wikidata:Q178430 chebi:25094 inchikey:KDXKERNSBIXSRK-UHFFFAOYSA-N pubchem.compound:5248709;pubchem.compound:866 chemspider:843 kegg.compound:C16440 2-Ketoglutaric acid Metabolite chebi:30915 "AKA 2-ketoglutarate, 2-oxoglutarate, 2-oxopentanedioic acid, α-ketoglutarate" wikidata:Q306140 chebi:30915 inchikey:KPGXRSRHYNQIFN-UHFFFAOYSA-N pubchem.compound:156274072;pubchem.compound:51 chemspider:50 hmdb:HMDB0000208 kegg.compound:C00026 Crotonyl CoA Metabolite chebi:57332 "AKA (E)-but-2-enoyl-CoA" wikidata:Q27124432 chebi:57332 inchikey:KFWWCMJSYSSPSK-PAXLJYGASA-J pubchem.compound:45266565 chemspider:26330708 NAD+ Metabolite chebi:15846 "" wikidata:Q26987253 chebi:15846 inchikey:BAWFJGJZGIEFAR-NNYOXOHSSA-O pubchem.compound:5893 chemspider:5682 hmdb:HMDB0000902 kegg.compound:C00003 D-2-Hydroxyglutaric acid Metabolite chebi:15801 "" wikidata:Q27098238 chebi:15801 inchikey:HWXBTNAVRSUOJR-GSVOUGTGSA-L pubchem.compound:5460200 chemspider:4573827 kegg.compound:C01087 2-aminoadipic semialdehyde Metabolite chebi:61515 "" wikidata:Q27131118 chebi:61515 inchikey:CRVYRJLIQHSUOQ-ZETCQYMHSA-N pubchem.compound:443994 chemspider:392029 kegg.compound:C12988 glutarylcarnitine Metabolite chebi:73040 "" wikidata:Q27140253 chebi:73040 inchikey:NXJAXUYOQLTISD-UHFFFAOYSA-N pubchem.compound:71464488;pubchem.compound:168314141 chemspider:21403175 hmdb:HMDB0240779 lipidmaps:LMFA07070091 3-hydroxyglutaryl CoA Metabolite pubchem.compound:445127 "" wikidata:Q307532 chebi:15467 inchikey:CABVTRNMFUVUDM-VRHQGPGLSA-N pubchem.compound:445127 chemspider:392859 hmdb:HMDB0001375 kegg.compound:C00356 lipidmaps:LMFA07050116 Antiquitin Protein ensembl:ENSG00000164904 "" ensembl:ENSG00000164904 ncbigene:501 hgnc.symbol:ALDH7A1 uniprot:A0A1B0GW77;uniprot:A0A1B0GW65;uniprot:A0A1B0GTY9;uniprot:P49419;uniprot:A0A1B0GTG2;uniprot:A0A1B0GTJ4;uniprot:A0A0J9YWF7;uniprot:A0A1B0GV49;uniprot:H0YHM6;uniprot:A0A0J9YWM6;uniprot:A0A1B0GUA1;uniprot:A0A0J9YWK1;uniprot:F8WDY6;uniprot:A0A1B0GVU0;uniprot:A0A1B0GW82;uniprot:F8WD33;uniprot:A0A1B0GUY0;uniprot:F8VVF2 IDH2 Protein ensembl:ENSG00000182054 "" ensembl:ENSG00000182054 ncbigene:3418 hgnc.symbol:IDH2 uniprot:H0YL11;uniprot:P48735;uniprot:H0YLL5 D-2-hydroxyglutarate dehydrogenase Protein uniprot:Q8N465 "" ensembl:ENSG00000180902 ncbigene:728294 hgnc.symbol:D2HGDH uniprot:G5E9E8;uniprot:H7C290;uniprot:H7C3L2;uniprot:F8WCF9;uniprot:B5MCV2;uniprot:H7C0N1;uniprot:H7C021;uniprot:Q8N465 L2HGDH Protein ensembl:ENSG00000087299 "" ensembl:ENSG00000087299 ncbigene:79944 hgnc.symbol:L2HGDH uniprot:Q9H9P8;uniprot:C9JVN9;uniprot:G3V272;uniprot:G3V3E2;uniprot:G3V5S1 L-malDH Protein uniprot:A0A024R4K3 "" ensembl:ENSG00000146701 ncbigene:4191 hgnc.symbol:MDH2 uniprot:U3KQ63;uniprot:A0A024R4K3;uniprot:G3XAL0;uniprot:P40926 Hydroxyacid-oxoacid transhydrogenase Protein uniprot:B4DFI7 "" ensembl:ENSG00000147576 ncbigene:137872 hgnc.symbol:ADHFE1 uniprot:F2Z3E5;uniprot:F2Z2N0;uniprot:Q8IWW8;uniprot:F2Z3D8;uniprot:B4DV11;uniprot:B4DFI7 Aminoacylase-2 Protein uniprot:A0A1B0GTG3 "Aka ACY1" ensembl:ENSG00000243989 ncbigene:95 hgnc.symbol:ACY1 uniprot:A0A1B0GU36;uniprot:F8WC59;uniprot:A0A1B0GVF7;uniprot:A0A1B0GU86;uniprot:C9JYZ0;uniprot:V9HWA0;uniprot:A0A1B0GTG3;uniprot:A0A1B0GUZ4;uniprot:A0A1B0GVG0;uniprot:A0A1B0GVZ3;uniprot:Q03154 Glutaryl-CoA dehydrogenase Protein uniprot:Q92947 "" ensembl:ENSG00000105607 ncbigene:2639 hgnc.symbol:GCDH uniprot:K7ES74;uniprot:K7EQ99;uniprot:K7ER63;uniprot:K7EKT3;uniprot:K7ERX1;uniprot:Q92947;uniprot:K7ESA6;uniprot:A0A024R7F9;uniprot:K7EKH1