Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI a-Ketoglutarate Metabolite chebi:16810 "aka 2-oxoglutarate" wikidata:Q27102088 chebi:16810;chebi:16810 inchikey:KPGXRSRHYNQIFN-UHFFFAOYSA-L Citrulline Metabolite chebi:57743 "Zwitterion needed for conversion to take place" wikidata:Q106345633 chebi:57743;chebi:57743 inchikey:RHGKLRLOHDJJDR-BYPYZUCNSA-N 1-Pyrroline-5-carboxylate Metabolite chebi:17388 "" wikidata:Q60998675 chebi:17388;chebi:17388 inchikey:DWAKNKKXGALPNW-BYPYZUCNSA-M Aspartate Metabolite chebi:29991 "(1-) charge needed for conversion to take place" wikidata:Q27104098 chebi:29991;chebi:29991 inchikey:CKLJMWTZIZZHCS-REOHCLBHSA-M Acetyl-CoA Metabolite chebi:57288 "(4-) charge needed for conversion to take place" wikidata:Q27124397 chebi:57288;chebi:57288 inchikey:ZSLZBFCDCINBPY-ZSJPKINUSA-J L-Glutamatey-semialdehyde Metabolite chebi:58066 "" wikidata:Q106345606 chebi:58066;chebi:58066 inchikey:KABXUUFDPUOJMW-BYPYZUCNSA-N Oxalacetate Metabolite chebi:16452 "" wikidata:Q27101912 chebi:16452;chebi:16452 inchikey:KHPXUQMNIQBQEV-UHFFFAOYSA-L Argininosuccinate Metabolite chebi:57472 "(1-) charge needed for conversion to take place" wikidata:Q27124717 chebi:57472;chebi:57472 inchikey:KDZOASGQNOPSCU-ZBHICJROSA-M Ornithine Metabolite chebi:46911 "(1) charge needed for conversion to take place" wikidata:Q27120725 chebi:46911;chebi:46911 inchikey:AHLPHDHHMVZTML-BYPYZUCNSA-O Urea Metabolite chebi:16199 "" wikidata:Q48318 chebi:16199;chebi:16199 inchikey:XSQUKJJJFZCRTK-UHFFFAOYSA-N Proline Metabolite chebi:60039 "" wikidata:Q106345478 chebi:60039;chebi:60039 inchikey:ONIBWKKTOPOVIA-BYPYZUCNSA-N Glutamate Metabolite chebi:29985 "(1-) charge needed for conversion to take place" wikidata:Q27104095 chebi:29985;chebi:29985 inchikey:WHUUTDBJXJRKMK-VKHMYHEASA-M Carbamoyl-phosphate Metabolite chebi:58228 "(2-) charge needed for conversion to take place" wikidata:Q27125628 chebi:58228;chebi:58228 inchikey:FFQKYPRQEYGKAF-UHFFFAOYSA-L Fumarate Metabolite chebi:29806 "(2-) charge needed for conversion to take place" wikidata:Q28529698 chebi:29806;chebi:29806 inchikey:VZCYOOQTPOCHFL-OWOJBTEDSA-L NH4+ Metabolite chebi:28938 "" wikidata:Q190901 chebi:28938;chebi:28938 inchikey:QGZKDVFQNNGYKY-UHFFFAOYSA-O N-acetylglutamate Metabolite chebi:44337 "(2-) charge needed for conversion to take place" wikidata:Q27104528 chebi:44337;chebi:44337 inchikey:RFMMMVDNIPUKGG-YFKPBYRVSA-L Pyruvate Metabolite chebi:15361 "" wikidata:Q27089397 chebi:15361;chebi:15361 inchikey:LCTONWCANYUPML-UHFFFAOYSA-M Lactate Metabolite chebi:16651 "" wikidata:Q27102013 chebi:16651;chebi:16651 inchikey:JVTAAEKCZFNVCJ-REOHCLBHSA-M Glutamine Metabolite chebi:58359 "Zwitterion needed for conversion to take place" wikidata:Q106345471 chebi:58359;chebi:58359 inchikey:ZDXPYRJPNDTMRX-VKHMYHEASA-N Alanine Metabolite chebi:57972 "" wikidata:Q106345485 chebi:57972;chebi:57972 inchikey:QNAYBMKLOCPYGJ-REOHCLBHSA-N Malate Metabolite chebi:15589 "" wikidata:Q27098126 chebi:15589;chebi:15589 inchikey:BJEPYKJPYRNKOW-REOHCLBHSA-L HCO3- Metabolite chebi:17544 "" wikidata:Q409202 chebi:17544;chebi:17544 inchikey:BVKZGUZCCUSVTD-UHFFFAOYSA-M Aspartate Metabolite chebi:29991 "(1-) charge needed for conversion to take place" wikidata:Q27104098 chebi:29991;chebi:29991 inchikey:CKLJMWTZIZZHCS-REOHCLBHSA-M Arginine Metabolite chebi:32682 "(1) charge needed for conversion to take place" wikidata:Q28529679 chebi:32682;chebi:32682 inchikey:ODKSFYDXXFIFQN-BYPYZUCNSA-O Ornithine Metabolite chebi:46911 "(1) charge needed for conversion to take place" wikidata:Q27120725 chebi:46911;chebi:46911 inchikey:AHLPHDHHMVZTML-BYPYZUCNSA-O Citrulline Metabolite chebi:57743 "Zwitterion needed for conversion to take place" wikidata:Q106345633 chebi:57743;chebi:57743 inchikey:RHGKLRLOHDJJDR-BYPYZUCNSA-N Oxalacetate Metabolite chebi:16452 "" wikidata:Q27101912 chebi:16452;chebi:16452 inchikey:KHPXUQMNIQBQEV-UHFFFAOYSA-L Glutamate Metabolite chebi:29985 "(1-) charge needed for conversion to take place" wikidata:Q27104095 chebi:29985;chebi:29985 inchikey:WHUUTDBJXJRKMK-VKHMYHEASA-M a-Ketoglutarate Metabolite chebi:16810 "aka 2-oxoglutarate" wikidata:Q27102088 chebi:16810;chebi:16810 inchikey:KPGXRSRHYNQIFN-UHFFFAOYSA-L Orotate Metabolite chebi:30839 "" wikidata:Q27104157 chebi:30839;chebi:30839 inchikey:PXQPEWDEAKTCGB-UHFFFAOYSA-M OMP Metabolite chebi:57538 "Orotidylic acid
(3-) charge needed for conversion to take place" wikidata:Q27124764 chebi:57538;chebi:57538 inchikey:KYOBSHFOBAOFBF-XVFCMESISA-K Uridine Metabolite chebi:16704 "" wikidata:Q422573 chebi:16704;chebi:16704 inchikey:DRTQHJPVMGBUCF-XVFCMESISA-N UMP Metabolite chebi:57865 "(2-) charge needed for conversion to take place" wikidata:Q27125012 chebi:57865;chebi:57865 inchikey:DJJCXFVJDGTHFX-XVFCMESISA-L Uracil Metabolite chebi:17568 "" wikidata:Q182990 chebi:17568;chebi:17568 inchikey:ISAKRJDGNUQOIC-UHFFFAOYSA-N Orotidine Metabolite chebi:25722 "" wikidata:Q10859719 chebi:25722;chebi:25722 inchikey:FKCRAVPPBFWEJD-XVFCMESISA-N Carbamoyl-phosphate Metabolite chebi:58228 "(2-) charge needed for conversion to take place" wikidata:Q27125628 chebi:58228;chebi:58228 inchikey:FFQKYPRQEYGKAF-UHFFFAOYSA-L NH4+ Metabolite chebi:28938 "" wikidata:Q190901 chebi:28938;chebi:28938 inchikey:QGZKDVFQNNGYKY-UHFFFAOYSA-O Nitric oxide Metabolite chebi:16480 "(1) charge needed for conversion to take place" wikidata:Q207843 chebi:16480;chebi:16480 inchikey:MWUXSHHQAYIFBG-UHFFFAOYSA-N Malate Metabolite chebi:15589 "" wikidata:Q27098126 chebi:15589;chebi:15589 inchikey:BJEPYKJPYRNKOW-REOHCLBHSA-L Oxalacetate Metabolite chebi:16452 "" wikidata:Q27101912 chebi:16452;chebi:16452 inchikey:KHPXUQMNIQBQEV-UHFFFAOYSA-L Glutamate Metabolite chebi:29985 "(1-) charge needed for conversion to take place" wikidata:Q27104095 chebi:29985;chebi:29985 inchikey:WHUUTDBJXJRKMK-VKHMYHEASA-M ARG1 Protein uniprot:P05089 "" ensembl:ENSG00000118520 ncbigene:383 hgnc.symbol:ARG1 uniprot:A0A5F9ZH78;uniprot:A0A5F9ZGN6;uniprot:P05089;uniprot:A0A5F9ZGY6 GLS2 Protein uniprot:Q9UI32 "" ensembl:ENSG00000135423 ncbigene:27165 hgnc.symbol:GLS2 uniprot:F8WBC9;uniprot:C9J3Q2;uniprot:F8WEU7;uniprot:A8K0A6;uniprot:A0A087X004;uniprot:F8WBL8;uniprot:G5E9X4;uniprot:Q9UI32;uniprot:E5G745 P5CS Protein uniprot:P30038 "" ensembl:ENSG00000159423 ncbigene:8659 hgnc.symbol:ALDH4A1 uniprot:Q5TF55;uniprot:A0A024RAC7;uniprot:P30038 Citrin(SLC25A13) Protein uniprot:Q9UJS0 "AKA CTLN2, SLC25A13, AGC2" ensembl:ENSG00000004864 ncbigene:10165 hgnc.symbol:SLC25A13 uniprot:R4GN64;uniprot:Q9UJS0 ASS1 Protein uniprot:P00966 "" ensembl:ENSG00000130707 ncbigene:445 hgnc.symbol:ASS1 uniprot:Q5T6L4;uniprot:Q5T6L6;uniprot:Q5T6L5;uniprot:P00966 ASL Protein uniprot:P04424 "" ensembl:ENSG00000126522 ncbigene:435 hgnc.symbol:ASL uniprot:F8W943;uniprot:P04424;uniprot:A0A5F9ZHC6;uniprot:A0A5F9ZI35;uniprot:A0A024RDL8;uniprot:A0A0S2Z316;uniprot:A0A5F9ZHM8 GDH Protein uniprot:P00367 "" ensembl:ENSG00000148672 ncbigene:2746 hgnc.symbol:GLUD1 uniprot:A0A804HJD7;uniprot:P00367;uniprot:A0A804HHS2;uniprot:A0A804HIA0;uniprot:A0A804HLC0;uniprot:A0A804HJH3;uniprot:A0A804HHU3;uniprot:A0A804HKE0;uniprot:A0A804HJZ0;uniprot:E9KL48 LDH Protein uniprot:P07195 "" ensembl:ENSG00000111716 ncbigene:3945 hgnc.symbol:LDHB uniprot:P07195;uniprot:Q5U077;uniprot:F5H793;uniprot:A0A5F9ZHM4;uniprot:A8MW50;uniprot:C9J7H8 ALT Protein uniprot:P24298 "" ensembl:ENSG00000167701 ncbigene:2875 hgnc.symbol:GPT uniprot:P24298 NAGS Protein uniprot:Q8N159 "" ensembl:ENSG00000161653 ncbigene:162417 hgnc.symbol:NAGS uniprot:K7EK11;uniprot:Q8N159 MDH Protein uniprot:P40925 "" ensembl:ENSG00000014641 ncbigene:4190 hgnc.symbol:MDH1 uniprot:C9IZI0;uniprot:B8ZZ51;uniprot:V9HWF2;uniprot:P40925;uniprot:B9A041;uniprot:C9JRL4;uniprot:C9JLV6;uniprot:F8WFC2;uniprot:A0A5K1VW95;uniprot:C9JF79 MDH2 Protein uniprot:P40926 "" ensembl:ENSG00000146701 ncbigene:4191 hgnc.symbol:MDH2 uniprot:U3KQ63;uniprot:A0A024R4K3;uniprot:G3XAL0;uniprot:P40926 OTC Protein uniprot:P00480 "" ensembl:ENSG00000036473 ncbigene:5009 hgnc.symbol:OTC uniprot:A0A2R8Y829;uniprot:P00480 OAT Protein uniprot:P04181 "" ensembl:ENSG00000065154 ncbigene:4942 hgnc.symbol:OAT uniprot:A0A140VJQ4;uniprot:P04181 SLC25A12 Protein uniprot:O75746 "AKA AGC1" ensembl:ENSG00000115840 ncbigene:8604 hgnc.symbol:SLC25A12 uniprot:B4DGK6;uniprot:H0YFB2;uniprot:F8W9J0;uniprot:O75746 AST2 Protein uniprot:P00505 "" ensembl:ENSG00000125166 ncbigene:2806 hgnc.symbol:GOT2 uniprot:H3BRE7;uniprot:P00505 FUM Protein uniprot:P07954 "" ensembl:ENSG00000091483 ncbigene:2271 hgnc.symbol:FH uniprot:A0A804HI24;uniprot:A0A804HKE6;uniprot:P07954;uniprot:A0A804HL52;uniprot:A0A0S2Z4C3 P5CR Protein uniprot:P32322 "" ensembl:ENSG00000183010 ncbigene:5831 hgnc.symbol:PYCR1 uniprot:A0A024R8U9;uniprot:J3QRZ0;uniprot:J3QL23;uniprot:J3QL24;uniprot:J3QKT4;uniprot:J3QL32;uniprot:J3QKT3;uniprot:J3KSA9;uniprot:J3KTA8;uniprot:J3KQ22;uniprot:E2QRB3;uniprot:J3QR88;uniprot:J3QLK9;uniprot:P32322 CPS1 Protein uniprot:P31327 "" ensembl:ENSG00000021826 ncbigene:1373 hgnc.symbol:CPS1 uniprot:P31327;uniprot:A0A024R454;uniprot:A0A669KBF2 ORNT1 Protein uniprot:Q9Y619 "Exchanges ornithine for citruline" ensembl:ENSG00000102743 ncbigene:10166 hgnc.symbol:SLC25A15 uniprot:Q5VZD9;uniprot:F2Z354;uniprot:Q9Y619 AST Protein uniprot:P17174 "" ensembl:ENSG00000120053 ncbigene:2805 hgnc.symbol:GOT1 uniprot:A0A140VK69;uniprot:P17174 iNOS Protein uniprot:P35228 "'Nitric oxide synthases (EC 1.14.13.39) (NOSs) are a family of enzymes catalyzing the production of nitric oxide (NO) from L-arginine. NO is an important cellular signaling molecule.' [https://en.wikipedia.org/wiki/Nitric_oxide_synthase#iNOS].
iNOS (inducible) is the protein active in hepatocytes, immune and cardiovascular system.
aka NOS2" ensembl:ENSG00000007171 ncbigene:4843 hgnc.symbol:NOS2 uniprot:A0A2R8YDS4;uniprot:P35228 nNOS Protein uniprot:P29475 "'Nitric oxide synthases (EC 1.14.13.39) (NOSs) are a family of enzymes catalyzing the production of nitric oxide (NO) from L-arginine. NO is an important cellular signaling molecule.' [https://en.wikipedia.org/wiki/Nitric_oxide_synthase#iNOS].
nNOS (neuronal) is the protein active in nervous tissue and skeletal muscle type II.
AKA NOS1" ensembl:ENSG00000089250 ncbigene:4842 hgnc.symbol:NOS1 uniprot:P29475;uniprot:B3VK56 eNOS Protein uniprot:P29474 "'Nitric oxide synthases (EC 1.14.13.39) (NOSs) are a family of enzymes catalyzing the production of nitric oxide (NO) from L-arginine. NO is an important cellular signaling molecule.' [https://en.wikipedia.org/wiki/Nitric_oxide_synthase#iNOS].
eNOS (endotheiliall) is the protein active in endothelium
AKA NOS3, cNOS" ensembl:ENSG00000164867 ncbigene:4846 hgnc.symbol:NOS3 uniprot:P29474;uniprot:H7C4V4;uniprot:E7ESA7