Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI ATP Metabolite chebi:30616 "" wikidata:Q27113900 chebi:30616;chebi:30616 inchikey:ZKHQWZAMYRWXGA-KQYNXXCUSA-J 3-keto-sphinganine Metabolite lipidmaps:LMSP01020002 "" wikidata:Q27073739 chebi:17862;chebi:17862 inchikey:KBUNOSOGGAARKZ-KRWDZBQOSA-N Palmitoyl-CoA Metabolite lipidmaps:LMFA07050360 "aka CoA(16:0)" wikidata:Q28797916 chebi:15525;chebi:15525 inchikey:MNBKLUUYKPBKDU-BBECNAHFSA-N Serine Metabolite pubchem.compound:5951 "" wikidata:Q183290 chebi:17115;chebi:17115 inchikey:MTCFGRXMJLQNBG-REOHCLBHSA-N Hexadecanal Metabolite lipidmaps:LMFA06000088 "" wikidata:Q27077978 chebi:17600;chebi:17600 inchikey:NIOYUNMRJMEDGI-UHFFFAOYSA-N Ethanolamine-phosphate Metabolite pubchem.compound:1015 "" wikidata:Q418826 chebi:17553;chebi:17553 inchikey:SUHOOTKUPISOBE-UHFFFAOYSA-N H2O Metabolite chebi:15377 "" wikidata:Q283 chebi:15377;chebi:15377 inchikey:XLYOFNOQVPJJNP-UHFFFAOYSA-N Sphingosine Metabolite lipidmaps:LMSP01010001 "" wikidata:Q46298 chebi:16393;chebi:16393 inchikey:WWUZIQQURGPMPG-KRWOKUGFSA-N Sphinganine Metabolite lipidmaps:LMSP01020001 "" wikidata:Q27088847 chebi:16566;chebi:16566 inchikey:OTKJDMGTUTTYMP-ZWKOTPCHSA-N Sphinganine-1-phosphate Metabolite lipidmaps:LMSP01050002 "" wikidata:Q27077062 chebi:16893;chebi:16893 inchikey:YHEDRJPUIRMZMP-ZWKOTPCHSA-N DH-Ceramide Metabolite lipidmaps:LMSP02020000 "" wikidata:Q60560163 chebi:139048;chebi:139048 Ceramide Metabolite lipidmaps:LMSP02010000 "" wikidata:Q60537688 chebi:52639;chebi:52639 Cer-1-P Metabolite lipidmaps:LMSP02050000 "" wikidata:Q38133997 chebi:16197;chebi:16197 DH-Cer-1-P Metabolite lipidmaps:LMSP020500A0 "" wikidata:Q60560137 SM Metabolite lipidmaps:LMSP0301 "" wikidata:Q423143 chebi:64583;chebi:64583 Glc-Cer Metabolite lipidmaps:LMSP0501AA00 "" wikidata:Q40205789 chebi:18368;chebi:18368 DH-SM Metabolite lipidmaps:LMSP030100A0 "" wikidata:Q37613317 Gal-Cer Metabolite lipidmaps:LMSP0501AC00 "" wikidata:Q40206202 chebi:18390;chebi:18390 Sphingosine-1-phosphate Metabolite lipidmaps:LMSP01050001 "" wikidata:Q418267 chebi:37550;chebi:37550 inchikey:DUYSYHSSBDVJSM-KRWOKUGFSA-N (2E)-hexadecenal Metabolite lipidmaps:LMFA06000089 "" wikidata:Q27102466 chebi:17585;chebi:17585 inchikey:KLJFYXOVGVXZKT-CCEZHUSRSA-N CoA(16:0) Metabolite lipidmaps:LMFA07050360 "" wikidata:Q28797916 chebi:15525;chebi:15525 inchikey:MNBKLUUYKPBKDU-BBECNAHFSA-N CoA(18:0) Metabolite chebi:15541 "" wikidata:Q15427851 chebi:15541;chebi:15541 inchikey:SIARJEKBADXQJG-LFZQUHGESA-N CoA(20:0) Metabolite chebi:15527 "" wikidata:Q27098079 chebi:15527;chebi:15527 inchikey:JYLSVNBJLYCSSW-IBYUJNRCSA-N CoA(22:0) Metabolite cas:24330-89-0 "" wikidata:Q27133642 chebi:65088;chebi:65088 inchikey:NDDZLVOCGALPLR-GNSUAQHMSA-N CoA(24:0) Metabolite cas:24305-30-4 "" wikidata:Q27123825 chebi:52974;chebi:52974 inchikey:MOYMQYZWIUKGGY-JBKAVQFISA-N CoA(24:1) Metabolite cas:88362-35-0 "" wikidata:Q27144452 chebi:74142;chebi:74142 inchikey:QHZAQVTVYPHLKK-YVBAAGQKSA-N CoA(16:0) Metabolite lipidmaps:LMFA07050360 "" wikidata:Q28797916 chebi:15525;chebi:15525 inchikey:MNBKLUUYKPBKDU-BBECNAHFSA-N CoA(18:0) Metabolite chebi:15541 "" wikidata:Q15427851 chebi:15541;chebi:15541 inchikey:SIARJEKBADXQJG-LFZQUHGESA-N CoA(20:0) Metabolite chebi:15527 "" wikidata:Q27098079 chebi:15527;chebi:15527 inchikey:JYLSVNBJLYCSSW-IBYUJNRCSA-N CoA(22:0) Metabolite cas:24330-89-0 "AKA 'Coenzyme A, S-​docosanoate'" wikidata:Q27133642 chebi:65088;chebi:65088 inchikey:NDDZLVOCGALPLR-GNSUAQHMSA-N CoA(24:0) Metabolite cas:24305-30-4 "AKA 'Coenzyme A, S-​(tetracosanoate)​'" wikidata:Q27123825 chebi:52974;chebi:52974 inchikey:MOYMQYZWIUKGGY-JBKAVQFISA-N CoA(24:1) Metabolite cas:88362-35-0 "AKA 'Coenzyme A, S-​(15Z)​-​15-​tetracosenoate'" wikidata:Q27144452 chebi:74142;chebi:74142 inchikey:QHZAQVTVYPHLKK-YVBAAGQKSA-N DH-Ceramide Metabolite lipidmaps:LMSP02020000 "" wikidata:Q60560163 chebi:139048;chebi:139048 DH-Ceramide Metabolite lipidmaps:LMSP02020000 "" wikidata:Q60560163 chebi:139048;chebi:139048 DH-Ceramide Metabolite lipidmaps:LMSP02020000 "" wikidata:Q60560163 chebi:139048;chebi:139048 DH-Ceramide Metabolite lipidmaps:LMSP02020000 "" wikidata:Q60560163 chebi:139048;chebi:139048 CoA(26:0) Metabolite cas:99313-57-2 "AKA 'Coenzyme A, S-​hexacosanoate'" wikidata:Q27123787 chebi:52966;chebi:52966 inchikey:FHLYYFPJDVYWQH-CPIGOPAHSA-N DH-Ceramide Metabolite lipidmaps:LMSP02020000 "" wikidata:Q60560163 chebi:139048;chebi:139048 CoA(26:0) Metabolite cas:99313-57-2 "" wikidata:Q27123787 chebi:52966;chebi:52966 inchikey:FHLYYFPJDVYWQH-CPIGOPAHSA-N ADP Metabolite chebi:456216 "" wikidata:Q27225748 chebi:456216;chebi:456216 inchikey:XTWYTFMLZFPYCI-KQYNXXCUSA-K CERK GeneProduct uniprot:Q8TCT0 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:223753" ensembl:ENSG00000100422 ncbigene:64781 hgnc.symbol:CERK uniprot:Q8TCT0;uniprot:F8WFD8;uniprot:A0A024R4U8 SGPP1 GeneProduct uniprot:Q9BX95 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q9JI99" ensembl:ENSG00000126821 ncbigene:81537 hgnc.symbol:SGPP1 uniprot:Q9BX95 ASAH1 GeneProduct uniprot:Q13510 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q9WV54" ensembl:ENSG00000104763 ncbigene:427 hgnc.symbol:ASAH1 uniprot:A0A1B0GTM3;uniprot:A0A1B0GTQ7;uniprot:A0A1B0GUQ5;uniprot:A0A1B0GW68;uniprot:A0A1B0GW66;uniprot:A0A1B0GV88;uniprot:A0A1B0GVG2;uniprot:A0A1B0GUG1;uniprot:A0A1B0GV06;uniprot:A0A1B0GU06;uniprot:A0A1B0GW48;uniprot:A0A1B0GTA6;uniprot:A0A1B0GUA4;uniprot:A0A1B0GVA3;uniprot:A0A1B0GVE7;uniprot:A0A1B0GUE3;uniprot:A0A1B0GV95;uniprot:E7EMM4;uniprot:A0A1B0GTZ5;uniprot:A0A1B0GU70;uniprot:A0A1B0GVA8;uniprot:A0A1B0GWC9;uniprot:A0A1B0GVC9;uniprot:A0A1B0GUP1;uniprot:A0A1B0GTX9;uniprot:Q13510;uniprot:A0A1B0GW30;uniprot:A0A1B0GUH5;uniprot:A0A1B0GUJ3;uniprot:A0A1B0GUJ2;uniprot:A0A1B0GVJ1;uniprot:A0A1B0GVL2;uniprot:A0A1B0GTP7;uniprot:A0A1B0GUB3;uniprot:A0A1B0GTD4;uniprot:A0A1B0GUW4;uniprot:A0A1B0GVY5;uniprot:A0A1B0GU62 SGMS1 GeneProduct uniprot:Q86VZ5 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:208449" ensembl:ENSG00000198964 ncbigene:259230 hgnc.symbol:SGMS1 uniprot:E6ZCI6;uniprot:U3KQ11;uniprot:R4GNI5;uniprot:Q86VZ5;uniprot:C0MHM2 SPHK2 GeneProduct uniprot:Q9NRA0 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q9JIA7" ensembl:ENSG00000063176 ncbigene:56848 hgnc.symbol:SPHK2 uniprot:M0R344;uniprot:M0QXX5;uniprot:M0R0E9;uniprot:A0A075B7A1;uniprot:E7ET12;uniprot:Q9NRA0;uniprot:M0QZP3;uniprot:A0A024QZH5;uniprot:E9PCV4 GBA1 GeneProduct uniprot:P04062 "" ensembl:ENSG00000177628 ncbigene:2629 hgnc.symbol:GBA uniprot:P04062;uniprot:A0A068F658 SPTLC1 GeneProduct uniprot:O15269 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:268656" ensembl:ENSG00000090054 ncbigene:10558 hgnc.symbol:SPTLC1 uniprot:A0A2R8Y4S0;uniprot:A0A024R277;uniprot:A0A2R8Y6A2;uniprot:A0A2R8Y763;uniprot:O15269 SPHK1 GeneProduct uniprot:Q9NYA1 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q8CI15" ensembl:ENSG00000176170 ncbigene:8877 hgnc.symbol:SPHK1 uniprot:K7EMA4;uniprot:Q9NYA1;uniprot:Q53ZR5;uniprot:K7EJ32 DEGS1 GeneProduct uniprot:O15121 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:13244" ensembl:ENSG00000143753 ncbigene:8560 hgnc.symbol:DEGS1 uniprot:E7EMA0;uniprot:O15121;uniprot:A0A024R3P1 SPTLC2 GeneProduct uniprot:O15270 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:P97363" ensembl:ENSG00000100596 ncbigene:9517 hgnc.symbol:SPTLC2 uniprot:A0A024R6H1;uniprot:H0YJ96;uniprot:H0YJV2;uniprot:O15270 DEGS2 GeneProduct uniprot:Q6QHC5 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:70059" ensembl:ENSG00000168350 ncbigene:123099 hgnc.symbol:DEGS2 uniprot:Q6QHC5;uniprot:G3V2F9 PLPP3 GeneProduct uniprot:O14495 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:67916" ensembl:ENSG00000162407 ncbigene:8613 hgnc.symbol:PLPP3 uniprot:O14495 SGPP2 GeneProduct uniprot:Q8IWX5 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q810K3" ensembl:ENSG00000163082 ncbigene:130367 hgnc.symbol:SGPP2 uniprot:Q8IWX5 GBA2 GeneProduct uniprot:Q9HCG7 "" ensembl:ENSG00000070610 ncbigene:57704 hgnc.symbol:GBA2 uniprot:Q9HCG7;uniprot:A0A0A0MRV1 GBA3 GeneProduct uniprot:Q9H227 "" Ppap2a Protein ncbigene:8611 "No homologues found for original id L:19012 Also, known as PLPP1" ensembl:ENSG00000067113 ncbigene:8611 hgnc.symbol:PLPP1 uniprot:A0A024QZS3;uniprot:O14494;uniprot:A0A024QZU7;uniprot:D6REC3 SGPL1 Protein ensembl:ENSG00000166224 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:20397" ensembl:ENSG00000166224 ncbigene:8879 hgnc.symbol:SGPL1 uniprot:H7BXL7;uniprot:O95470 UGCG Protein uniprot:Q16739 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:22234" ensembl:ENSG00000148154 ncbigene:7357 hgnc.symbol:UGCG uniprot:Q16739;uniprot:A0A024R157 KDSR Protein uniprot:Q06136 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q6GV12" ensembl:ENSG00000119537 ncbigene:2531 hgnc.symbol:KDSR uniprot:A0A024R292;uniprot:A0A2R8YF70;uniprot:Q06136;uniprot:A0A2R8Y7U3;uniprot:K7ERC8;uniprot:K7EQS7 CERS4 Protein ensembl:ENSG00000090661 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:67260" ensembl:ENSG00000090661 ncbigene:79603 hgnc.symbol:CERS4 uniprot:H0YKC9;uniprot:H0YKS3;uniprot:H0YMY6;uniprot:H0YKR4;uniprot:H0YLY3;uniprot:Q9HA82;uniprot:H0YN04;uniprot:H0YNR6 CERS4 Protein ensembl:ENSG00000090661 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:67260" ensembl:ENSG00000090661 ncbigene:79603 hgnc.symbol:CERS4 uniprot:H0YKC9;uniprot:H0YKS3;uniprot:H0YMY6;uniprot:H0YKR4;uniprot:H0YLY3;uniprot:Q9HA82;uniprot:H0YN04;uniprot:H0YNR6 CERS6 Protein ensembl:ENSG00000172292 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:241447" ensembl:ENSG00000172292 ncbigene:253782 hgnc.symbol:CERS6 uniprot:Q6ZMG9 SMPD1 Protein uniprot:P17405 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:20597" ensembl:ENSG00000166311 ncbigene:6609 hgnc.symbol:SMPD1 uniprot:P17405;uniprot:G3V1E1;uniprot:E9PPK6;uniprot:H0YEP5;uniprot:E9PL59;uniprot:E9PQT3 SGMS2 Protein uniprot:Q8NHU3 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:74442" ensembl:ENSG00000164023 ncbigene:166929 hgnc.symbol:SGMS2 uniprot:E5RGG5;uniprot:A0A024RDH4;uniprot:E5RJ63;uniprot:E5RJU3;uniprot:Q8NHU3 Ppap2c Protein ncbigene:8612 "Also known as PLPP2" ensembl:ENSG00000141934 ncbigene:8612 hgnc.symbol:PLPP2 uniprot:O43688;uniprot:K7ENH4;uniprot:K7EMK9;uniprot:A0A0J9YXA3 UGT8 Protein ensembl:ENSG00000174607 "EC:2.4.1.47" ensembl:ENSG00000174607 ncbigene:7368 hgnc.symbol:UGT8 uniprot:D6RFW2;uniprot:Q16880 CERS1 Protein ensembl:ENSG00000223802 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:P27545" ensembl:ENSG00000223802 ncbigene:10715 hgnc.symbol:CERS1 uniprot:M0R0T2;uniprot:P27544;uniprot:Q5XG75 CERS4 Protein ensembl:ENSG00000090661 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:67260" ensembl:ENSG00000090661 ncbigene:79603 hgnc.symbol:CERS4 uniprot:H0YKC9;uniprot:H0YKS3;uniprot:H0YMY6;uniprot:H0YKR4;uniprot:H0YLY3;uniprot:Q9HA82;uniprot:H0YN04;uniprot:H0YNR6 CERS2 Protein ensembl:ENSG00000143418 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = L:76893" ensembl:ENSG00000143418 ncbigene:29956 hgnc.symbol:CERS2 uniprot:Q96G23;uniprot:H0YLQ6;uniprot:H0YNU7;uniprot:Q5SZE4;uniprot:Q5SZE3;uniprot:H0YKH6;uniprot:Q5SZE2;uniprot:Q5SZE1 CERS3 Protein ensembl:ENSG00000154227 "Homology Mapping from Mus musculus to Homo sapiens: Original ID = S:Q1A3B0" ensembl:ENSG00000154227 ncbigene:204219 hgnc.symbol:CERS3 uniprot:Q8IU89;uniprot:H0YMG6;uniprot:H0YN05