Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI PubChem ChemSpider HMDB KEGG LipidMaps heme b Metabolite chebi:60344 "" wikidata:Q27127201 chebi:60344 inchikey:KABFMIBPWCXCRK-RGGAHWMASA-J;inchikey:RNQMHXMGXVQRMV-UHFFFAOYSA-L pubchem.compound:53356659;pubchem.compound:76021505 chemspider:559353;chemspider:28532758 hmdb:HMDB0003178 2Fe-2S Metabolite chebi:30408 "" wikidata:Q312085 chebi:30408 kegg.compound:C00824 UQCC3 GeneProduct ensembl:ENSG00000204922 "" ensembl:ENSG00000204922 ncbigene:790955 hgnc.symbol:UQCC3 uniprot:Q6UW78 UQCC2 GeneProduct ensembl:ENSG00000137288 "" ensembl:ENSG00000137288 ncbigene:84300 hgnc.symbol:UQCC2 uniprot:Q5TAQ0;uniprot:V5IRT4;uniprot:Q9BRT2 UQCRH GeneProduct ensembl:ENSG00000173660 "" ensembl:ENSG00000173660 ncbigene:7388 hgnc.symbol:UQCRH uniprot:A0A087WTF2;uniprot:P07919;uniprot:A0A087X2B9 UQCRC2 GeneProduct ensembl:ENSG00000140740 "" ensembl:ENSG00000140740 ncbigene:7385 hgnc.symbol:UQCRC2 uniprot:H3BUI9;uniprot:H3BP04;uniprot:H3BUE4;uniprot:A0A087WVZ4;uniprot:H3BSJ9;uniprot:H3BRG4;uniprot:P22695 LYRM7 GeneProduct ensembl:ENSG00000186687 "" ensembl:ENSG00000186687 ncbigene:90624 hgnc.symbol:LYRM7 uniprot:Q5U5X0;uniprot:D6R994;uniprot:D6RBV5 UQCR11 GeneProduct ensembl:ENSG00000127540 "" ensembl:ENSG00000127540 ncbigene:10975 hgnc.symbol:UQCR11 uniprot:O14957 UQCRB GeneProduct ensembl:ENSG00000156467 "" ensembl:ENSG00000156467 ncbigene:7381 hgnc.symbol:UQCRB uniprot:E5RHG9;uniprot:E5RIT7;uniprot:P14927;uniprot:B7Z2R2 UQCRC1 GeneProduct ensembl:ENSG00000010256 "" ensembl:ENSG00000010256 ncbigene:7384 hgnc.symbol:UQCRC1 uniprot:F8WER5;uniprot:F8WEF1;uniprot:P31930 MT-CYB GeneProduct ensembl:ENSG00000198727 "" ensembl:ENSG00000198727 ncbigene:4519 hgnc.symbol:MT-CYB uniprot:P00156;uniprot:Q0ZFD6 UQCRQ GeneProduct ensembl:ENSG00000164405 "" ensembl:ENSG00000164405 ncbigene:27089 hgnc.symbol:UQCRQ uniprot:O14949 UQCRFS1 GeneProduct ensembl:ENSG00000169021 "" ensembl:ENSG00000169021 ncbigene:7386 hgnc.symbol:UQCRFS1 uniprot:P47985 CYC1 GeneProduct ensembl:ENSG00000179091 "" ensembl:ENSG00000179091 ncbigene:1537 hgnc.symbol:CYC1 uniprot:P08574 BCS1L GeneProduct ensembl:ENSG00000074582 "" ensembl:ENSG00000074582 ncbigene:617 hgnc.symbol:BCS1L uniprot:C9JAS4;uniprot:H7BZF6;uniprot:C9J8G3;uniprot:Q9Y276;uniprot:A0A2R8Y7T3;uniprot:A0A024R445;uniprot:C9J4Q9;uniprot:H7C492;uniprot:C9J1S9 UQCC1 GeneProduct ensembl:ENSG00000101019 "" ensembl:ENSG00000101019 ncbigene:55245 hgnc.symbol:UQCC1 uniprot:B1AKV2;uniprot:B1AKV3;uniprot:B1AKV4;uniprot:F6UTR7;uniprot:H7C611;uniprot:Q9NVA1;uniprot:Q3KRB6;uniprot:D6RDV2;uniprot:H7C3C3;uniprot:B1AKV6;uniprot:F8WAM1;uniprot:H7BZM2;uniprot:F8WCR2 TTC19 GeneProduct ensembl:ENSG00000011295 "" ensembl:ENSG00000011295 ncbigene:54902 hgnc.symbol:TTC19 uniprot:K7ERR1;uniprot:A0A024RD83;uniprot:K7EJA1;uniprot:K7EKH7;uniprot:Q6DKK2;uniprot:K7ELX2;uniprot:K7EKS0 UQCR10 GeneProduct ensembl:ENSG00000184076 "" ensembl:ENSG00000184076 ncbigene:29796 hgnc.symbol:UQCR10 uniprot:Q9UDW1