Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI pyruvate Metabolite chebi:15361 wikidata:Q27089397 chebi:15361;chebi:15361 inchikey:LCTONWCANYUPML-UHFFFAOYSA-M Apo-ACC Metabolite chebi:29969 aka apo-[methylmalonyl-CoA:pyruvate carboxytransferase] chebi:29969 propanoyl-CoA Metabolite chebi:57392 aka propionyl-CoA wikidata:Q27124603 chebi:57392;chebi:57392 inchikey:QAQREVBBADEHPA-IEXPHMLFSA-J leucine Metabolite chebi:25017 wikidata:Q60662890 chebi:25017;chebi:25017 inchikey:ROHFNLRQFUQHCH-UHFFFAOYSA-N oxaloacetate Metabolite chebi:16452 wikidata:Q27101912 chebi:16452;chebi:16452 inchikey:KHPXUQMNIQBQEV-UHFFFAOYSA-L 3-methylglutaconyl-CoA Metabolite chebi:57346 aka trans-3-methylglutaconyl-CoA wikidata:Q27124446 chebi:57346;chebi:57346 inchikey:ZMMFWDHIXCPOHZ-XRYKKJIBSA-I 3-methylcrotonyl-COA Metabolite chebi:57344 aka 3-methylbut-2-enoyl-CoA wikidata:Q27124444 chebi:57344;chebi:57344 inchikey:BXIPALATIYNHJN-ZMHDXICWSA-J Dietary and otherprotein-bound biotin Metabolite chebi:16615 wikidata:Q27101999 chebi:16615;chebi:16615 inchikey:XFLVBMBRLSCJAI-ZKWXMUAHSA-N Biocytin Metabolite wikidata:Q864247 biotin covalantly bound to lysine wikidata:Q864247 chebi:27870;chebi:27870 inchikey:BAQMYDQNMFBZNA-MNXVOIDGSA-N Lysine Metabolite chebi:25094 wikidata:Q178430 chebi:25094;chebi:25094 inchikey:KDXKERNSBIXSRK-UHFFFAOYSA-N free biotin Metabolite chebi:15956 wikidata:Q181354 chebi:15956;chebi:15956 inchikey:YBJHBAHKTGYVGT-ZKWXMUAHSA-N Acetyl-CoA Metabolite chebi:57288 wikidata:Q27124397 chebi:57288;chebi:57288 inchikey:ZSLZBFCDCINBPY-ZSJPKINUSA-J Biotin (free pool) Metabolite chebi:15956 wikidata:Q181354 chebi:15956;chebi:15956 inchikey:YBJHBAHKTGYVGT-ZKWXMUAHSA-N Malonyl-CoA Metabolite chebi:57384 wikidata:Q27124561 chebi:57384;chebi:57384 inchikey:LTYOQGRJFJAKNA-DVVLENMVSA-I holo-ACC Metabolite chebi:83144 aka holo-[methylmalonyl-CoA:pyruvate carboxytransferase] chebi:83144 Apo-PCC Metabolite chebi:29969 aka apo-[propionyl-CoA:carbon-dioxide ligase (ADP-forming)] chebi:29969 holo-PCC Metabolite chebi:83144 aka holo-[propionyl-CoA:carbon-dioxide ligase (ADP-forming)] chebi:83144 Apo-MCC Metabolite chebi:29969 aka apo-[3-methylcrotonoyl-CoA:carbon-dioxide ligase (ADP-forming)] chebi:29969 holo-MCC Metabolite chebi:83144 aka holo-[3-methylcrotonoyl-CoA:carbon-dioxide ligase (ADP-forming)] chebi:83144 Apo-PC Metabolite chebi:29969 aka pyruvate carboxylase chebi:29969 holo-PC Metabolite chebi:83144 aka pyruvate carboxylase chebi:83144 Biotin Metabolite chebi:15956 wikidata:Q181354 chebi:15956;chebi:15956 inchikey:YBJHBAHKTGYVGT-ZKWXMUAHSA-N methylmanoyl-CoA Metabolite chebi:57327 wikidata:Q27124427 chebi:57327;chebi:57327 inchikey:MZFOKIKEPGUZEN-IBNUZSNCSA-I PC Protein uniprot:P11498 aka pyruvate carboxylase ensembl:ENSG00000173599 ncbigene:5091 hgnc.symbol:PC uniprot:A0A494C016;uniprot:P11498;uniprot:A0A494C101;uniprot:A0A494BZT5;uniprot:A0A494C0T2;uniprot:A0A024R5C5;uniprot:E9PRE7 MCCC1 Protein uniprot:Q96RQ3 ensembl:ENSG00000078070 ncbigene:56922 hgnc.symbol:MCCC1 uniprot:F2Z2Z7;uniprot:F2Z3E2;uniprot:F8WF46;uniprot:E9PG35;uniprot:E9PHF7;uniprot:G5E9X5;uniprot:F8WDI3;uniprot:A0A0S2Z693;uniprot:Q96RQ3 Biotinidase (BTD) Protein uniprot:P43251 ensembl:ENSG00000169814 ncbigene:686 hgnc.symbol:BTD uniprot:A0A5F9ZHF5;uniprot:A0A5F9ZHR1;uniprot:A0A5F9ZH97;uniprot:C9JSN9;uniprot:A0A5F9ZH15;uniprot:A0A5F9ZHE9;uniprot:P43251;uniprot:A0A5F9ZH57;uniprot:A0A5F9ZH80;uniprot:A0A2R8Y5J9 HLCS Protein uniprot:P50747 aka Holocarboxylase Synthetase ensembl:ENSG00000159267 ncbigene:3141 hgnc.symbol:HLCS uniprot:A0A0C4DG27;uniprot:A0A6Q8PFK4;uniprot:P50747;uniprot:C9JCQ9 ACC1(cytosol) Protein uniprot:Q13085 aka acetyl-CoA carboxylase ensembl:ENSG00000278540 ncbigene:31 hgnc.symbol:ACACA uniprot:A0A087WWN5;uniprot:A0A087WYS8;uniprot:A0A087X0W4;uniprot:A0A087X2F8;uniprot:A0A0C4DGT1;uniprot:Q59FY4;uniprot:A0A087WYK6;uniprot:A0A087X126;uniprot:Q13085;uniprot:A0A087WVR6;uniprot:A0A024R0Y2 ACC2(mitochondrial) Protein uniprot:O00763 aka acetyl-CoA carboxylase ensembl:ENSG00000076555 ncbigene:32 hgnc.symbol:ACACB uniprot:F8W8T8;uniprot:A0A087WUA1;uniprot:O00763;uniprot:F5H5C3;uniprot:S4R3S7;uniprot:H0YGH5 MCCC2 Protein uniprot:Q9HCC0 ensembl:ENSG00000131844 ncbigene:64087 hgnc.symbol:MCCC2 uniprot:A0A140VK29;uniprot:A0A0S2Z5R4;uniprot:D6R9R1;uniprot:D6RD67;uniprot:D6RDF7;uniprot:Q9HCC0 PCCA Protein uniprot:P05165 ensembl:ENSG00000175198 ncbigene:5095 hgnc.symbol:PCCA uniprot:Q5JVH2;uniprot:A0A1B0GU58;uniprot:A0A1B0GWA1;uniprot:H0Y5U0;uniprot:A0A1B0GUX9;uniprot:H0Y4B9;uniprot:Q5JTW6;uniprot:A0A1B0GTR1;uniprot:A0A1B0GWI4;uniprot:H0Y798;uniprot:P05165;uniprot:A0A2R8Y725 PCCB Protein uniprot:P05166 ensembl:ENSG00000114054 ncbigene:5096 hgnc.symbol:PCCB uniprot:E7ENC1;uniprot:E7EX59;uniprot:P05166;uniprot:C9JVY9;uniprot:C9JVW9;uniprot:C9JQS9;uniprot:F8WBI9;uniprot:H7C5C9;uniprot:E7EUY3;uniprot:E9PEC3;uniprot:E7ETT1;uniprot:C9JAW3;uniprot:E7ETT4;uniprot:E9PDR0