Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI a ubiquinone Metabolite chebi:16389 "" wikidata:Q2981798 chebi:16389;chebi:16389 FADH2 Metabolite chebi:58307 "" wikidata:Q26998317 chebi:58307;chebi:58307 inchikey:YPZRHBJKEMOYQH-UYBVJOGSSA-L 6 PP Metabolite chebi:33019 "diphosphate" wikidata:Q27115222 chebi:33019;chebi:33019 inchikey:XPPKVPWEQAFLFU-UHFFFAOYSA-K FMN Metabolite chebi:58210 "aka flavin mononucleotide" wikidata:Q27125576 chebi:58210;chebi:58210 inchikey:FVTCRASFADXXNN-SCRDCRAPSA-K;inchikey:ANKZYBDXHMZBDK-SCRDCRAPSA-K trans-decaprenyl-PP Metabolite chebi:60721 "aka all-trans-decaprenyl diphosphate" wikidata:Q27128561 chebi:60721;chebi:60721 inchikey:FSCYHDCTHRVSKN-CMVHWAPMSA-K CoQ10 Metabolite chebi:46245 "" wikidata:Q321285 chebi:46245;chebi:46245 inchikey:ACTIUHUUMQJHFO-UPTCCGCDSA-N 6 IPP Metabolite chebi:128769 "aka isopentenyl diphosphate" wikidata:Q27221807 chebi:128769;chebi:128769 inchikey:NUHSROFQTUXZQQ-UHFFFAOYSA-K Farnesyl-PP Metabolite chebi:175763 "aka Farnesyl PyroPhosphate" wikidata:Q27225693 chebi:175763;chebi:175763 inchikey:VWFJDQUYCIWHTN-YFVJMOTDSA-K AMP Metabolite chebi:16027 "cofactor [https://en.wikipedia.org/wiki/Electron-transferring_flavoprotein]" wikidata:Q318369 chebi:16027;chebi:16027 inchikey:UDMBCSSLTHHNCD-KQYNXXCUSA-N RIB Metabolite chebi:17015 "" wikidata:Q130365 chebi:17015;chebi:17015 inchikey:AUNGANRZJHBGPY-SCRDCRAPSA-N FMN Metabolite chebi:17621 "" wikidata:Q376061 chebi:17621;chebi:17621 inchikey:FVTCRASFADXXNN-SCRDCRAPSA-N RIB Metabolite chebi:17015 "aka riboflavin" wikidata:Q130365 chebi:17015;chebi:17015 inchikey:AUNGANRZJHBGPY-SCRDCRAPSA-N FAD Metabolite chebi:16238 "" wikidata:Q28746 chebi:16238;chebi:16238 inchikey:VWWQXMAJTJZDQX-UYBVJOGSSA-N FAD Metabolite chebi:57692 "aka flavin adenine dinucleotide" wikidata:Q27124863 chebi:57692;chebi:57692 inchikey:IMGVNJNCCGXBHD-UYBVJOGSSA-K a ubiquinol Metabolite chebi:17976 "" wikidata:Q39906287 chebi:17976;chebi:17976 FAD Metabolite chebi:57692 "" wikidata:Q27124863 chebi:57692;chebi:57692 inchikey:IMGVNJNCCGXBHD-UYBVJOGSSA-K FAD Metabolite chebi:57692 "aka flavin adenine dinucleotide
cofactor [https://en.wikipedia.org/wiki/Electron-transferring_flavoprotein]" wikidata:Q27124863 chebi:57692;chebi:57692 inchikey:IMGVNJNCCGXBHD-UYBVJOGSSA-K PHB Metabolite chebi:30763 "" wikidata:Q229970 chebi:30763;chebi:30763 inchikey:FJKROLUGYXJWQN-UHFFFAOYSA-N DHB Metabolite chebi:64136 "" wikidata:Q27133055 chebi:64136;chebi:64136 inchikey:CMPNJZREBHCPHN-LTNIBBDRSA-N all-E-10PrP2 Metabolite chebi:61011 "" wikidata:Q27130563 chebi:61011;chebi:61011 inchikey:FSCYHDCTHRVSKN-CMVHWAPMSA-N PPi Metabolite chebi:29888 "" wikidata:Q411092 chebi:29888;chebi:29888 inchikey:XPPKVPWEQAFLFU-UHFFFAOYSA-N FAD Metabolite chebi:16238 "" wikidata:Q28746 chebi:16238;chebi:16238 inchikey:VWWQXMAJTJZDQX-UYBVJOGSSA-N DHDB Metabolite chebi:50775 "" wikidata:Q27122231 chebi:50775;chebi:50775 inchikey:HGWUGDIATLOPBN-BHZQGFRMSA-N Q10H2 Metabolite chebi:64183 "aka ubiquinol-10" wikidata:Q28529714 chebi:64183;chebi:64183 inchikey:QNTNKSLOFHEFPK-UPTCCGCDSA-N DMQ10H2 Metabolite chebi:64181 "" wikidata:Q27133102 chebi:64181;chebi:64181 inchikey:XCOXSBLQZPFVGK-RGIWONJESA-N DeMQ10H2 Metabolite chebi:64182 "" wikidata:Q27133103 chebi:64182;chebi:64182 inchikey:VLMQNHNMQVLPQI-AVRCVIBKSA-N MHDB Metabolite chebi:50776 "" wikidata:Q27122232 chebi:50776;chebi:50776 inchikey:WCQCNOIKXGNDLX-RDSVHMIISA-N DMPhOH Metabolite chebi:50774 "" wikidata:Q27122230 chebi:50774;chebi:50774 inchikey:FYLLWSGFAAQKHU-GBBROCKZSA-N MDMQ10H2 Metabolite chebi:64180 "" wikidata:Q27133101 chebi:64180;chebi:64180 inchikey:LIOKNOIJMJKVCG-RDSVHMIISA-N Fe2+ Metabolite chebi:29033 "" wikidata:Q428946 chebi:29033;chebi:29033 inchikey:CWYNVVGOOAEACU-UHFFFAOYSA-N Trans-nonaprenyl-PP Metabolite chebi:58391 "aka all-trans-nonaprenyl diphosphate" wikidata:Q27125752 chebi:58391;chebi:58391 inchikey:IVLBHBFTRNVIAP-MEGGAXOGSA-K 7 PP Metabolite chebi:33019 "diphosphate" wikidata:Q27115222 chebi:33019;chebi:33019 inchikey:XPPKVPWEQAFLFU-UHFFFAOYSA-K 7 IPP Metabolite chebi:128769 "aka isopentenyl diphosphate" wikidata:Q27221807 chebi:128769;chebi:128769 inchikey:NUHSROFQTUXZQQ-UHFFFAOYSA-K CETF GeneProduct interpro:IPR014730 "aka electron transfer flavoprotein complex" ETFDH GeneProduct ensembl:ENSG00000171503 "" ensembl:ENSG00000171503 ncbigene:2110 hgnc.symbol:ETFDH uniprot:A0A804HK66;uniprot:A0A804HI48;uniprot:A0A804HJT7;uniprot:A0A804HL84;uniprot:A0A804HKY7;uniprot:A0A804HK08;uniprot:Q16134;uniprot:A0A804HK05;uniprot:A0A804HJK8;uniprot:A0A804HI73;uniprot:A0A804HL81;uniprot:A0A804HI80;uniprot:A0A804HKB8;uniprot:B4DEQ0;uniprot:A0A804HI70 PDSS1 Protein uniprot:Q5T2R2 "" ensembl:ENSG00000148459 ncbigene:23590 hgnc.symbol:PDSS1 uniprot:H0YEE6;uniprot:Q5T2R2 Riboflavin kinase Protein uniprot:Q969G6 "EC: 2.7.1.26 (according to Rhea)" ensembl:ENSG00000135002 ncbigene:55312 hgnc.symbol:RFK uniprot:Q969G6;uniprot:H7C4G0 CABC1 Protein uniprot:Q8NI60 "aka COQ8A, ADCK3.
atypical kinase, substrate specificity unknown [https://www.uniprot.org/uniprot/Q8NI60]" ensembl:ENSG00000163050 ncbigene:56997 hgnc.symbol:COQ8A uniprot:Q8NI60 APTX Protein uniprot:Q7Z2E3 "" ensembl:ENSG00000137074 ncbigene:54840 hgnc.symbol:APTX uniprot:F8WBM3;uniprot:A0A5F9ZGW5;uniprot:A0A5F9ZI51;uniprot:Q6JV79;uniprot:A0A0A0MRW7;uniprot:Q7Z2E3;uniprot:A0A5K1VW80;uniprot:C9J8U3;uniprot:F8WBD6;uniprot:A0A5K1VW64 FAD synthetase Protein uniprot:Q8NFF5 "aka FLAD1, EC 2.7.7.2 [https://en.wikipedia.org/wiki/FMN_adenylyltransferase]" ensembl:ENSG00000160688 ncbigene:80308 hgnc.symbol:FLAD1 uniprot:Q5T196;uniprot:Q5T191;uniprot:Q8NFF5;uniprot:Q5T190 ETFDH Protein uniprot:Q16134 "" ensembl:ENSG00000171503 ncbigene:2110 hgnc.symbol:ETFDH uniprot:A0A804HK66;uniprot:A0A804HI48;uniprot:A0A804HJT7;uniprot:A0A804HL84;uniprot:A0A804HKY7;uniprot:A0A804HK08;uniprot:Q16134;uniprot:A0A804HK05;uniprot:A0A804HJK8;uniprot:A0A804HI73;uniprot:A0A804HL81;uniprot:A0A804HI80;uniprot:A0A804HKB8;uniprot:B4DEQ0;uniprot:A0A804HI70 SLC52A1 Protein uniprot:Q9NWF4 "" ensembl:ENSG00000132517 ncbigene:55065 hgnc.symbol:SLC52A1 uniprot:F5H5Y1;uniprot:Q9NWF4 SLC52A2 Protein uniprot:Q9HAB3 "" ensembl:ENSG00000185803 ncbigene:79581 hgnc.symbol:SLC52A2 uniprot:E9PJC1;uniprot:Q9HAB3;uniprot:A0A6Q8PGB9;uniprot:A0A6Q8PGE2;uniprot:A0A6Q8PFH5;uniprot:E9PKE4;uniprot:A0A6Q8PG35;uniprot:E9PPS0;uniprot:E9PIX2;uniprot:A0A6Q8PFQ5;uniprot:A0A6Q8PHF8;uniprot:E9PRC3 SLC52A3 Protein uniprot:SLC52A3 "" ETFA Protein uniprot:P13804 "" ensembl:ENSG00000140374 ncbigene:2108 hgnc.symbol:ETFA uniprot:H0YLU7;uniprot:H0YM12;uniprot:A0A0S2Z3M4;uniprot:H0YK49;uniprot:H0YMU8;uniprot:A0A0S2Z3L0;uniprot:H0YL83;uniprot:P13804;uniprot:H3BV91;uniprot:H0YKF0;uniprot:J3KN60 ETFB Protein uniprot:38117 "" COQ2 Protein uniprot:Q96H96 "" ensembl:ENSG00000173085 ncbigene:27235 hgnc.symbol:COQ2 uniprot:E2QRG7;uniprot:A0A1D8H0A6;uniprot:H0YAI0;uniprot:E7EPM7;uniprot:Q96H96 COQ6 Protein uniprot:Q9Y2Z9 "" ensembl:ENSG00000119723 ncbigene:51004 hgnc.symbol:COQ6 uniprot:G3V2L5;uniprot:Q9Y2Z9;uniprot:G3V3A1;uniprot:A0A0D9SFJ1;uniprot:G3V434;uniprot:G3V3L0;uniprot:G3V4A6 COQ7 Protein uniprot:Q99807 "" ensembl:ENSG00000167186 ncbigene:10229 hgnc.symbol:COQ7 uniprot:H3BP28;uniprot:Q99807;uniprot:H3BS11;uniprot:H3BSZ3;uniprot:H3BTN8;uniprot:I3L1T0 COQ9 Protein uniprot:O75208 "" ensembl:ENSG00000088682 ncbigene:57017 hgnc.symbol:COQ9 uniprot:H3BPY0;uniprot:H3BPC6;uniprot:A0A024R6U3;uniprot:H3BNT2;uniprot:H3BPW3;uniprot:H3BRC0;uniprot:H3BSJ5;uniprot:O75208;uniprot:H3BVA5 PDSS2 Protein uniprot:Q86YH6 "" ensembl:ENSG00000164494 ncbigene:57107 hgnc.symbol:PDSS2 uniprot:Q5JRD6;uniprot:Q86YH6