Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI DG-O Metabolite lipidmaps:LMGL02020000 "" Acyl-CoA Metabolite lipidmaps:LMFA07050000 "" wikidata:Q2699537 chebi:17984;chebi:17984 Alkyl-DHAP Metabolite lipidmaps:LMGP22020000 "" Fatty acid Metabolite lipidmaps:LMFA01010000 "" wikidata:Q61476 chebi:35366;chebi:35366 LPA Metabolite lipidmaps:LMGP10050000 "" wikidata:Q22082936 chebi:16975;chebi:16975 Acyl-DHAP Metabolite lipidmaps:LMGP22010000 "" Coenzyme A Metabolite chebi:15346 "" wikidata:Q407635 chebi:15346;chebi:15346 inchikey:RGJOEKWQDUBAIZ-DRCCLKDXSA-N;inchikey:RGJOEKWQDUBAIZ-IBOSZNHHSA-N LPA-O Metabolite lipidmaps:LMGP10060000 "" GalEAG Metabolite lipidmaps:LMGL050200A0 "" PC-O Metabolite lipidmaps:LMGP01020000 "" PE-O Metabolite lipidmaps:LMGP02020000 "" PA-O Metabolite lipidmaps:LMGP10020000 "" PE-P Metabolite lipidmaps:LMGP02030000 "AKA PE-Plasmalogen" Fatty alcohol Metabolite lipidmaps:LMFA05000000 "" DHAP Metabolite chebi:16108 "aka dihydroxyacetone phosphate" wikidata:Q416915 chebi:16108;chebi:16108 inchikey:GNGACRATGGDKBX-UHFFFAOYSA-N Seminolipid Metabolite lipidmaps:LMGL05020000 "" Acyl-CoA Metabolite lipidmaps:LMFA07050000 "" wikidata:Q2699537 chebi:17984;chebi:17984 Coenzyme A Metabolite chebi:15346 "" wikidata:Q407635 chebi:15346;chebi:15346 inchikey:RGJOEKWQDUBAIZ-DRCCLKDXSA-N;inchikey:RGJOEKWQDUBAIZ-IBOSZNHHSA-N Alkyl-DHAP Metabolite lipidmaps:LMGP22020000 "" Acyl-CoA Metabolite lipidmaps:LMFA07050000 "" wikidata:Q2699537 chebi:17984;chebi:17984 Fatty acid Metabolite chebi:57560 "" wikidata:Q74237672 chebi:57560;chebi:57560 Fatty alcohol Metabolite lipidmaps:LMFA05000000 "" Acyl-DHAP Metabolite lipidmaps:LMGP22010000 "" PexRAP GeneProduct uniprot:Q6IAN0 "AKA an acyl/alkyl DHAP reductase; 'identified this gene as dhrs7b and renamed the protein PexRAP (for peroxisomal reductase activating PPARĪ³)' [PMID:28523433]" ensembl:ENSG00000109016 ncbigene:25979 hgnc.symbol:DHRS7B uniprot:J3QKT1;uniprot:J3KRS1;uniprot:J3QLK1;uniprot:Q6IAN0;uniprot:A0A0C4DGQ8;uniprot:J3QLJ8 ACS GeneProduct eccode:6.2.1.1 "AKA acyl-CoA synthetase; composed of two subunits." LPIN3 GeneProduct uniprot:Q9BQK8 "" ensembl:ENSG00000132793 ncbigene:64900 hgnc.symbol:LPIN3 uniprot:H0Y5E1;uniprot:Q9BQK8 GNPAT GeneProduct uniprot:O15228 "AKA glyceronephosphate O-acyltransferase" ensembl:ENSG00000116906 ncbigene:8443 hgnc.symbol:GNPAT uniprot:Q5TBH6;uniprot:O15228;uniprot:A0A2R8YH69;uniprot:Q5TBH8 PEX1 GeneProduct uniprot:O43933 "" ensembl:ENSG00000127980 ncbigene:5189 hgnc.symbol:PEX1 uniprot:A0A0C4DG33;uniprot:H7BZH3;uniprot:O43933 ARSA GeneProduct uniprot:P15289 "" ensembl:ENSG00000100299 ncbigene:410 hgnc.symbol:ARSA uniprot:V9GYR0;uniprot:A0A0C4DFZ2;uniprot:P15289 PEDS1 GeneProduct uniprot:A5PLL7 "" ensembl:ENSG00000240849 ncbigene:387521 hgnc.symbol:PEDS1 uniprot:A5PLL7;uniprot:F8W924;uniprot:F8WBY2;uniprot:Q5TGE2 LPCAT1 GeneProduct uniprot:Q8NF37 "" ensembl:ENSG00000153395 ncbigene:79888 hgnc.symbol:LPCAT1 uniprot:Q8NF37 AGPS GeneProduct uniprot:O00116 "" ensembl:ENSG00000018510 ncbigene:8540 hgnc.symbol:AGPS uniprot:A0A1B0GWA2;uniprot:A0A7P0T9C9;uniprot:A0A7P0T8Q7;uniprot:B7Z3Q4;uniprot:A0A7P0TAL3;uniprot:A0A7P0T857;uniprot:A0A7P0T984;uniprot:O00116;uniprot:A0A7P0TAU9;uniprot:B8ZZ81;uniprot:A0A2R8YEL0;uniprot:A0A7P0TA54 PEX5L GeneProduct uniprot:Q8IYB4 "AKA Pex5 long isoform; 'While both the long and short Pex5 isoforms recognize PTS1-containing proteins, Pex5L is a co-receptor with Pex7 for the import of PTS2-containing proteins, and its loss results only in impaired PTS2-tagged protein import' [PMID:28523433]. AGPS contains a PTS2 domain (type-2 peroxisomal targeting signal). [PMID:31751594]" ensembl:ENSG00000114757 ncbigene:51555 hgnc.symbol:PEX5L uniprot:C9IZ09;uniprot:C9JUZ5;uniprot:C9JB85;uniprot:Q8IYB4;uniprot:C9JZE2 PEX7 GeneProduct uniprot:O00628 "AKA peroxisomal import receptor for proteins, including AGPS [PMID:28523433]" ensembl:ENSG00000112357 ncbigene:5191 hgnc.symbol:PEX7 uniprot:A0A7I2V2W7;uniprot:O00628;uniprot:A0A7I2V3V6;uniprot:A0A7I2YQJ4;uniprot:Q5TDQ5;uniprot:Q6FGN1;uniprot:A0A7I2V2J8 GAL3ST1 GeneProduct uniprot:Q99999 "EC 2.8.2.11 " ensembl:ENSG00000128242 ncbigene:9514 hgnc.symbol:GAL3ST1 uniprot:C9J2X7;uniprot:C9JTV3;uniprot:C9JU54;uniprot:C9J3S3;uniprot:C9J993;uniprot:C9K037;uniprot:C9JN55;uniprot:C9JGL4;uniprot:A0A024R1D7;uniprot:C9J6M2;uniprot:C9J2M1;uniprot:Q99999;uniprot:C9JE31;uniprot:C9JKD7;uniprot:C9J4I2;uniprot:C9JLB5;uniprot:C9JIS3;uniprot:C9JYD7 LPIN1 GeneProduct uniprot:Q14693 "" ensembl:ENSG00000134324 ncbigene:23175 hgnc.symbol:LPIN1 uniprot:C9J278;uniprot:A0A0A0MS66;uniprot:C9IYP2;uniprot:H7C3T1;uniprot:Q14693 UGT8 GeneProduct uniprot:Q16880 "" ensembl:ENSG00000174607 ncbigene:7368 hgnc.symbol:UGT8 uniprot:D6RFW2;uniprot:Q16880 LPIN2 GeneProduct uniprot:Q92539 "" ensembl:ENSG00000101577 ncbigene:9663 hgnc.symbol:LPIN2 uniprot:J3QQN0;uniprot:Q92539 CEPT1 GeneProduct uniprot:Q9Y6K0 "" ensembl:ENSG00000134255 ncbigene:10390 hgnc.symbol:CEPT1 uniprot:Q9Y6K0;uniprot:A1PL14 FAR1 GeneProduct uniprot:Q8WVX9 "AKA fatty acyl-CoA reductase." ensembl:ENSG00000197601 ncbigene:84188 hgnc.symbol:FAR1 uniprot:E9PPB8;uniprot:E9PNW8;uniprot:Q8WVX9 FAR2 GeneProduct uniprot:Q96K12 "AKA fatty acyl-CoA reductase." ensembl:ENSG00000064763 ncbigene:55711 hgnc.symbol:FAR2 uniprot:F8VPF2;uniprot:Q96K12;uniprot:A0A024RAW7;uniprot:H0YHP1;uniprot:F8VX60;uniprot:H0YIE0 AGPS GeneProduct uniprot:O00116 "" ensembl:ENSG00000018510 ncbigene:8540 hgnc.symbol:AGPS uniprot:A0A1B0GWA2;uniprot:A0A7P0T9C9;uniprot:A0A7P0T8Q7;uniprot:B7Z3Q4;uniprot:A0A7P0TAL3;uniprot:A0A7P0T857;uniprot:A0A7P0T984;uniprot:O00116;uniprot:A0A7P0TAU9;uniprot:B8ZZ81;uniprot:A0A2R8YEL0;uniprot:A0A7P0TA54 PEX7 GeneProduct uniprot:O00628 "AKA peroxisomal import receptor for proteins, including AGPS [PMID:28523433]" ensembl:ENSG00000112357 ncbigene:5191 hgnc.symbol:PEX7 uniprot:A0A7I2V2W7;uniprot:O00628;uniprot:A0A7I2V3V6;uniprot:A0A7I2YQJ4;uniprot:Q5TDQ5;uniprot:Q6FGN1;uniprot:A0A7I2V2J8 PEX3 GeneProduct uniprot:P56589 "" ensembl:ENSG00000034693 ncbigene:8504 hgnc.symbol:PEX3 uniprot:Q7Z6V3;uniprot:P56589 PEX16 GeneProduct uniprot:Q9Y5Y5 "" ensembl:ENSG00000121680 ncbigene:9409 hgnc.symbol:PEX16 uniprot:E9PSC6;uniprot:E9PQW0;uniprot:Q9Y5Y5;uniprot:E9PP98;uniprot:E9PLS4;uniprot:E9PMS3;uniprot:E9PMM3 PEX19 GeneProduct uniprot:P40855 "" ensembl:ENSG00000162735 ncbigene:5824 hgnc.symbol:PEX19 uniprot:B7Z8B3;uniprot:H0YDY4;uniprot:Q5QNY5;uniprot:P40855;uniprot:E9PS71;uniprot:A0A0S2Z497;uniprot:E9PPB4 UNIDENTIFIED Protein eccode:1.1.1.101 "Putative EC number as found in RHGEA entry https://www.rhea-db.org/rhea/36175"