Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI H2O Metabolite hmdb:HMDB0002111 "" chebi:15377;chebi:15377 inchikey:XLYOFNOQVPJJNP-UHFFFAOYSA-N H2O Metabolite hmdb:HMDB0002111 "" chebi:15377;chebi:15377 inchikey:XLYOFNOQVPJJNP-UHFFFAOYSA-N C1S GeneProduct ncbigene:716 "" ensembl:ENSG00000182326 ncbigene:716 hgnc.symbol:C1S uniprot:C9IZP8;uniprot:B5MCV4;uniprot:F8WCZ6;uniprot:C9JY52;uniprot:H0Y5D1;uniprot:P09871;uniprot:F5H7T4 C1QB GeneProduct ncbigene:713 "" ensembl:ENSG00000173369 ncbigene:713 hgnc.symbol:C1QB uniprot:D6R934;uniprot:A0A0A0MSV6;uniprot:D6RGJ1 C1R GeneProduct ensembl:ENSG00000159403 "" ensembl:ENSG00000159403 ncbigene:715 hgnc.symbol:C1R uniprot:F5GWL0;uniprot:B4DPQ0;uniprot:F5H1V0;uniprot:F5H6Y3;uniprot:F5H2D0;uniprot:F5H3A3;uniprot:F5H3N3;uniprot:A0A3B3ISR2;uniprot:A0A3B3ITU4;uniprot:F5H1N6 C1QA GeneProduct ncbigene:712 "update: C1QA HUMAN" ensembl:ENSG00000173372 ncbigene:712 hgnc.symbol:C1QA uniprot:X6RLJ0;uniprot:A0A024RAG6;uniprot:P02745 C1QG GeneProduct ncbigene:714 "update C1QC HUMAN" ensembl:ENSG00000159189 ncbigene:714 hgnc.symbol:C1QC uniprot:P02747;uniprot:A0A024RAA7 C8A GeneProduct ncbigene:731 "" ensembl:ENSG00000157131 ncbigene:731 hgnc.symbol:C8A uniprot:P07357 MASP2 GeneProduct ncbigene:10747 "" ensembl:ENSG00000009724 ncbigene:10747 hgnc.symbol:MASP2 uniprot:O00187 C2A GeneProduct ncbigene:717 "" ensembl:ENSG00000166278 ncbigene:717 hgnc.symbol:C2 uniprot:H0Y3H6;uniprot:H0Y868;uniprot:Q5JP69;uniprot:B4DQI1;uniprot:P06681;uniprot:F8WCJ9;uniprot:E9PDZ0;uniprot:C9JYQ5;uniprot:A2ABG0;uniprot:F2Z3N2;uniprot:F2Z306;uniprot:Q5ST52;uniprot:Q8N6L6 C3 GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 C9 GeneProduct ncbigene:735 "" ensembl:ENSG00000113600 ncbigene:735 hgnc.symbol:C9 uniprot:P02748 C8B GeneProduct ncbigene:732 "" ensembl:ENSG00000021852 ncbigene:732 hgnc.symbol:C8B uniprot:P07358 C6 GeneProduct ncbigene:729 "" ensembl:ENSG00000039537 ncbigene:729 hgnc.symbol:C6 uniprot:C9JC72;uniprot:C9JX36;uniprot:P13671 C4B GeneProduct ncbigene:721 "" ensembl:ENSG00000224389 ncbigene:721 hgnc.symbol:C4B uniprot:A0A3B3ISA6;uniprot:A0A3B3ISD7;uniprot:F5GXS0;uniprot:P0C0L5 DAF GeneProduct ncbigene:1604 "" ensembl:ENSG00000196352 ncbigene:1604 hgnc.symbol:CD55 uniprot:P08174;uniprot:A0A2R8YDY3;uniprot:H3BLV0;uniprot:B1AP15;uniprot:A0A2R8YEC5;uniprot:A0A2R8Y4B4;uniprot:B1AP13 C4A GeneProduct ncbigene:720 "" ensembl:ENSG00000244731 ncbigene:110384692;ncbigene:720 hgnc.symbol:C4A uniprot:P0C0L4 C7 GeneProduct ncbigene:730 "" ensembl:ENSG00000112936 ncbigene:730 hgnc.symbol:C7 uniprot:P10643 C5 GeneProduct ncbigene:727 "" ensembl:ENSG00000106804 ncbigene:727 hgnc.symbol:C5 uniprot:P01031 C2 GeneProduct ncbigene:717 "" ensembl:ENSG00000166278 ncbigene:717 hgnc.symbol:C2 uniprot:H0Y3H6;uniprot:H0Y868;uniprot:Q5JP69;uniprot:B4DQI1;uniprot:P06681;uniprot:F8WCJ9;uniprot:E9PDZ0;uniprot:C9JYQ5;uniprot:A2ABG0;uniprot:F2Z3N2;uniprot:F2Z306;uniprot:Q5ST52;uniprot:Q8N6L6 C4B GeneProduct ncbigene:721 "" ensembl:ENSG00000224389 ncbigene:721 hgnc.symbol:C4B uniprot:A0A3B3ISA6;uniprot:A0A3B3ISD7;uniprot:F5GXS0;uniprot:P0C0L5 C3B GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 C2A GeneProduct ncbigene:717 "" ensembl:ENSG00000166278 ncbigene:717 hgnc.symbol:C2 uniprot:H0Y3H6;uniprot:H0Y868;uniprot:Q5JP69;uniprot:B4DQI1;uniprot:P06681;uniprot:F8WCJ9;uniprot:E9PDZ0;uniprot:C9JYQ5;uniprot:A2ABG0;uniprot:F2Z3N2;uniprot:F2Z306;uniprot:Q5ST52;uniprot:Q8N6L6 C4B GeneProduct ncbigene:721 "" ensembl:ENSG00000224389 ncbigene:721 hgnc.symbol:C4B uniprot:A0A3B3ISA6;uniprot:A0A3B3ISD7;uniprot:F5GXS0;uniprot:P0C0L5 C5B GeneProduct ncbigene:727 "" ensembl:ENSG00000106804 ncbigene:727 hgnc.symbol:C5 uniprot:P01031 C1QB GeneProduct ncbigene:713 "" ensembl:ENSG00000173369 ncbigene:713 hgnc.symbol:C1QB uniprot:D6R934;uniprot:A0A0A0MSV6;uniprot:D6RGJ1 C1QG GeneProduct ncbigene:714 "update C1QC HUMAN" ensembl:ENSG00000159189 ncbigene:714 hgnc.symbol:C1QC uniprot:P02747;uniprot:A0A024RAA7 C1QA GeneProduct ncbigene:712 "update: C1QA HUMAN" ensembl:ENSG00000173372 ncbigene:712 hgnc.symbol:C1QA uniprot:X6RLJ0;uniprot:A0A024RAG6;uniprot:P02745 C1R GeneProduct ensembl:ENSG00000159403 "" ensembl:ENSG00000159403 ncbigene:715 hgnc.symbol:C1R uniprot:F5GWL0;uniprot:B4DPQ0;uniprot:F5H1V0;uniprot:F5H6Y3;uniprot:F5H2D0;uniprot:F5H3A3;uniprot:F5H3N3;uniprot:A0A3B3ISR2;uniprot:A0A3B3ITU4;uniprot:F5H1N6 C1S GeneProduct ncbigene:716 "" ensembl:ENSG00000182326 ncbigene:716 hgnc.symbol:C1S uniprot:C9IZP8;uniprot:B5MCV4;uniprot:F8WCZ6;uniprot:C9JY52;uniprot:H0Y5D1;uniprot:P09871;uniprot:F5H7T4 C8G GeneProduct ncbigene:733 "" ensembl:ENSG00000176919 ncbigene:733 hgnc.symbol:C8G uniprot:A0A3B3ITK5;uniprot:P07360;uniprot:A0A3B3ITY0 MASP1 GeneProduct ncbigene:5648 "" ensembl:ENSG00000127241 ncbigene:5648 hgnc.symbol:MASP1 uniprot:F8W876;uniprot:P48740;uniprot:C9JMA2;uniprot:C9JLU5;uniprot:C9J1C7 C3B GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 CFBb GeneProduct ncbigene:629 "" ensembl:ENSG00000243649 ncbigene:629 hgnc.symbol:CFB uniprot:A0A1U9X7H8;uniprot:P00751;uniprot:F8WBL9;uniprot:H7C5H1 C3 GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 C3 GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 CFB GeneProduct ncbigene:629 "" ensembl:ENSG00000243649 ncbigene:629 hgnc.symbol:CFB uniprot:A0A1U9X7H8;uniprot:P00751;uniprot:F8WBL9;uniprot:H7C5H1 CFD GeneProduct ncbigene:1675 "" ensembl:ENSG00000197766 ncbigene:1675 hgnc.symbol:CFD uniprot:P00746;uniprot:K7ERG9 C3B GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 CFP GeneProduct ncbigene:5199 "" ensembl:ENSG00000126759 ncbigene:5199 hgnc.symbol:CFP uniprot:P27918;uniprot:C9J7V5;uniprot:A0A0S2Z4I5;uniprot:E9PAQ1 C3B GeneProduct ncbigene:718 "" ensembl:ENSG00000125730 ncbigene:718 hgnc.symbol:C3 uniprot:M0QXZ3;uniprot:V9HWA9;uniprot:P01024;uniprot:M0R1Q1;uniprot:M0R0Q9;uniprot:M0QYC8 CFBb GeneProduct ncbigene:629 "" ensembl:ENSG00000243649 ncbigene:629 hgnc.symbol:CFB uniprot:A0A1U9X7H8;uniprot:P00751;uniprot:F8WBL9;uniprot:H7C5H1 CFP GeneProduct ncbigene:5199 "" ensembl:ENSG00000126759 ncbigene:5199 hgnc.symbol:CFP uniprot:P27918;uniprot:C9J7V5;uniprot:A0A0S2Z4I5;uniprot:E9PAQ1 C5 GeneProduct ncbigene:727 "" ensembl:ENSG00000106804 ncbigene:727 hgnc.symbol:C5 uniprot:P01031