Label Type Identifier Comment Ensembl NCBI gene HGNC UniProt Wikidata ChEBI InChI PubChem ChemSpider HMDB KEGG LipidMaps protoporphyrinogen IX Metabolite chebi:57307 "" wikidata:Q27124410 chebi:57307 inchikey:UHSGPDMIQQYNAX-UHFFFAOYSA-L pubchem.compound:20849104 chemspider:20171538 delta-aminolevulinate Metabolite chemspider:10447539 "" wikidata:Q27108930 chebi:12109 inchikey:ZGXJTSGNIOSYLO-UHFFFAOYSA-M pubchem.compound:16722119 chemspider:10447539 O₂ Metabolite hmdb:HMDB0001377 "" chebi:15379 inchikey:MYMOFIZGZYHOMD-UHFFFAOYSA-N pubchem.compound:977 chemspider:952 hmdb:HMDB0001377 kegg.compound:C00007 porphobilinogen Metabolite cas:487-90-1 "" wikidata:Q421178 chebi:17381 inchikey:QSHWIQZFGQKFMA-UHFFFAOYSA-N pubchem.compound:1021 chemspider:995 hmdb:HMDB0000245 kegg.compound:C00931 NH₃ Metabolite hmdb:HMDB0000051 "" chebi:16134 inchikey:QGZKDVFQNNGYKY-UHFFFAOYSA-N pubchem.compound:222 chemspider:217 hmdb:HMDB0000051 kegg.compound:C00014 H⁺ Metabolite pubchem.compound:1038 "" wikidata:Q506710 chebi:15378 inchikey:GPRLSGONYQIRFK-UHFFFAOYSA-N pubchem.compound:1038 chemspider:1010 hmdb:HMDB0059597 kegg.compound:C00080 H₂O₂ Metabolite hmdb:HMDB0003125 "" chebi:16240 inchikey:MHAJPDPJQMAIIY-UHFFFAOYSA-N pubchem.compound:784 chemspider:763 hmdb:HMDB0003125 kegg.compound:C00027 CoA Metabolite hmdb:HMDB0001423 "" chebi:15346 inchikey:RGJOEKWQDUBAIZ-IBOSZNHHSA-N pubchem.compound:87642 chemspider:79067 hmdb:HMDB0001423 kegg.compound:C00010 uroporphyrinogen III Metabolite cas:1976-85-8 "" wikidata:Q897727 chebi:15437 inchikey:HUHWZXWWOFSFKF-UHFFFAOYSA-N pubchem.compound:1179 chemspider:1146 hmdb:HMDB0001086 kegg.compound:C01051 CO₂ Metabolite hmdb:HMDB0001967 "" chebi:16526 inchikey:CURLTUGMZLYLDI-UHFFFAOYSA-N pubchem.compound:280 chemspider:274 hmdb:HMDB0001967 kegg.compound:C00011 succinyl-CoA Metabolite hmdb:HMDB0001022 "" chebi:15380 inchikey:VNOYUJKHFWYWIR-ITIYDSSPSA-N pubchem.compound:92133 chemspider:83179 hmdb:HMDB0001022 kegg.compound:C00091 Glycine Metabolite hmdb:HMDB0000123 "" chebi:15428 inchikey:DHMQDGOQFOQNFH-UHFFFAOYSA-N pubchem.compound:750 chemspider:730 hmdb:HMDB0000123 kegg.compound:C00037 H₂O Metabolite hmdb:HMDB0002111 "" chebi:15377 inchikey:XLYOFNOQVPJJNP-UHFFFAOYSA-N pubchem.compound:962 chemspider:937 hmdb:HMDB0002111 kegg.compound:C00001 coproporphyrinogen III Metabolite cas:2624-63-7 "" wikidata:Q2468481 chebi:15439 inchikey:NIUVHXTXUXOFEB-UHFFFAOYSA-N pubchem.compound:321 chemspider:315 hmdb:HMDB0001261 kegg.compound:C03263 Porphobilinogen Metabolite hmdb:HMDB0000245 "" chebi:17381 inchikey:QSHWIQZFGQKFMA-UHFFFAOYSA-N pubchem.compound:1021 chemspider:995 hmdb:HMDB0000245 kegg.compound:C00931 hydroxymethylbilane Metabolite chebi:16645 "" wikidata:Q2639442 chebi:16645 inchikey:WDFJYRZCZIUBPR-UHFFFAOYSA-N pubchem.compound:788 chemspider:767 hmdb:HMDB0001137 kegg.compound:C01024 Fe²⁺ Metabolite pubchem.compound:27284 "" wikidata:Q428946 chebi:29033 inchikey:CWYNVVGOOAEACU-UHFFFAOYSA-N pubchem.compound:27284 chemspider:25394 hmdb:HMDB0000692 kegg.compound:C14818 protoheme Metabolite cas:14875-96-8 "" wikidata:Q620084 chebi:26355 inchikey:KABFMIBPWCXCRK-RGGAHWMASA-L pubchem.compound:444098 chemspider:16739950 hmdb:HMDB0003178 kegg.compound:C00032 protoporphyrin IX Metabolite cas:553-12-8 "" wikidata:Q619815 chebi:15430 inchikey:KSFOVUSSGSKXFI-UJJXFSCMSA-N;inchikey:ZCFFYALKHPIRKJ-UHFFFAOYSA-N pubchem.compound:4971 chemspider:3022121;chemspider:4800;chemspider:10469486;chemspider:23975886;chemspider:21430808 hmdb:HMDB0000241 kegg.compound:C02191 ALAS2 GeneProduct ncbigene:212 "" ensembl:ENSG00000158578 ncbigene:212 hgnc.symbol:ALAS2 uniprot:A0A2R8Y782;uniprot:H0Y6R3;uniprot:P22557;uniprot:A0A2R8Y6N3;uniprot:A0A2R8Y836;uniprot:A0A2R8Y6R4 FECH GeneProduct ncbigene:2235 "" ensembl:ENSG00000066926 ncbigene:2235 hgnc.symbol:FECH uniprot:A0A499FJN5;uniprot:K7EJX5;uniprot:K7ELX4;uniprot:P22830;uniprot:K7EJM8 PPOX GeneProduct ncbigene:5498 "" ensembl:ENSG00000143224 ncbigene:5498 hgnc.symbol:PPOX uniprot:A0A494C146;uniprot:F5H1I5;uniprot:P50336;uniprot:F5H825;uniprot:F5GZT7;uniprot:A0A494C134;uniprot:A0A1W2PPA5;uniprot:A0A494C0M9;uniprot:A0A494C1M8;uniprot:H0YFP3;uniprot:A0A1W2PRF9;uniprot:A0A494C0L4;uniprot:D3DVG2;uniprot:A0A494C0C8;uniprot:A0A494C0D4;uniprot:A0A1W2PNH4;uniprot:A0A1W2PQM0;uniprot:H0YFE1 CPOX GeneProduct ncbigene:1371 "" ensembl:ENSG00000080819 ncbigene:1371 hgnc.symbol:CPOX uniprot:D6RER6;uniprot:P36551 HMBS GeneProduct ncbigene:3145 "" ensembl:ENSG00000256269 ncbigene:3145 hgnc.symbol:HMBS uniprot:A0A1W2PNU5;uniprot:F5H0P4;uniprot:F5H345;uniprot:A0A8I5KXV4;uniprot:F5H4W5;uniprot:F5H4Y7;uniprot:A0A3F2YNY7;uniprot:P08397;uniprot:F5H226;uniprot:A0A3B3IT17;uniprot:F5GY90;uniprot:F5H4X2;uniprot:A0A3B3IU34;uniprot:A0A3B3IU56;uniprot:A0A3B3IRR1 ALAS1 GeneProduct ncbigene:211 "" ensembl:ENSG00000023330 ncbigene:211 hgnc.symbol:ALAS1 uniprot:Q5JAM2;uniprot:H7C4H7;uniprot:H7C5B0;uniprot:P13196 ALAD GeneProduct ncbigene:210 "" ensembl:ENSG00000148218 ncbigene:210 hgnc.symbol:ALAD uniprot:B7ZBK6;uniprot:P13716;uniprot:A0A140VJL9;uniprot:B7ZBK8;uniprot:B7ZBK7 UROS GeneProduct ncbigene:7390 "" ensembl:ENSG00000188690 ncbigene:7390 hgnc.symbol:UROS uniprot:Q5T3L7;uniprot:A0A087X021;uniprot:Q5T3L9;uniprot:Q5T3L8;uniprot:A0A3B3IUC8;uniprot:A0A0S2Z4T8;uniprot:A0A087WZB7;uniprot:P10746;uniprot:A0A3B3ISL9;uniprot:A0A3B3ISM6;uniprot:A0A3B3ITJ2;uniprot:A0A087WUV7;uniprot:A0A3B3IS76;uniprot:A0A3B3IS33;uniprot:A0A3B3IU75;uniprot:A0A3B3ISX6 UROD GeneProduct ncbigene:7389 "" ensembl:ENSG00000126088 ncbigene:7389 hgnc.symbol:UROD uniprot:A0A494C0P4;uniprot:A0A494C0S8;uniprot:A0A494BZV1;uniprot:A0A494C1T3;uniprot:A0A1B0GVN9;uniprot:A0A494C007;uniprot:A0A494C0Q8;uniprot:P06132;uniprot:A0A494BZY8;uniprot:A0A494C1D8;uniprot:Q5T446;uniprot:A0A1B0GVZ4;uniprot:A0A494C085;uniprot:H0Y5R6